Detalhe da pesquisa
1.
AAV9 Gene Therapy Increases Lifespan and Treats Pathological and Behavioral Abnormalities in a Mouse Model of CLN8-Batten Disease.
Mol Ther
; 29(1): 162-175, 2021 01 06.
Artigo
Inglês
| MEDLINE | ID: mdl-33010819
2.
Peroxymonosulfate Rapidly Inactivates the Disease-Associated Prion Protein.
Environ Sci Technol
; 50(13): 7095-105, 2016 07 05.
Artigo
Inglês
| MEDLINE | ID: mdl-27247993
3.
Sortilin inhibition treats multiple neurodegenerative lysosomal storage disorders.
bioRxiv
; 2023 Sep 22.
Artigo
Inglês
| MEDLINE | ID: mdl-37790379
4.
Early postnatal administration of an AAV9 gene therapy is safe and efficacious in CLN3 disease.
Front Genet
; 14: 1118649, 2023.
Artigo
Inglês
| MEDLINE | ID: mdl-37035740
5.
Fate of prions in soil: a review.
J Environ Qual
; 40(2): 449-61, 2011.
Artigo
Inglês
| MEDLINE | ID: mdl-21520752
6.
Chemical Inactivation of Prions Is Altered by Binding to the Soil Mineral Montmorillonite.
ACS Infect Dis
; 7(4): 859-870, 2021 04 09.
Artigo
Inglês
| MEDLINE | ID: mdl-33787209
7.
A CLN6-CLN8 complex recruits lysosomal enzymes at the ER for Golgi transfer.
J Clin Invest
; 130(8): 4118-4132, 2020 08 03.
Artigo
Inglês
| MEDLINE | ID: mdl-32597833
8.
Absolute quantification of prion protein (90-231) using stable isotope-labeled chymotryptic peptide standards in a LC-MRM AQUA workflow.
J Am Soc Mass Spectrom
; 23(9): 1522-33, 2012 Sep.
Artigo
Inglês
| MEDLINE | ID: mdl-22714949