Detalhe da pesquisa
1.
Mitochondria in disease: changes in shapes and dynamics.
Trends Biochem Sci
; 49(4): 346-360, 2024 Apr.
Artigo
Inglês
| MEDLINE | ID: mdl-38402097
2.
Functional diversity among cardiolipin binding sites on the mitochondrial ADP/ATP carrier.
EMBO J
; 2024 Jun 05.
Artigo
Inglês
| MEDLINE | ID: mdl-38839991
3.
Mitochondrial compartmentalization: emerging themes in structure and function.
Trends Biochem Sci
; 46(11): 902-917, 2021 11.
Artigo
Inglês
| MEDLINE | ID: mdl-34244035
4.
Adenine nucleotide translocase regulates airway epithelial metabolism, surface hydration and ciliary function.
J Cell Sci
; 134(4)2021 02 25.
Artigo
Inglês
| MEDLINE | ID: mdl-33526710
5.
Diverse mitochondrial abnormalities in a new cellular model of TAFFAZZIN deficiency are remediated by cardiolipin-interacting small molecules.
J Biol Chem
; 297(3): 101005, 2021 09.
Artigo
Inglês
| MEDLINE | ID: mdl-34314685
6.
Tafazzin deficiency impairs CoA-dependent oxidative metabolism in cardiac mitochondria.
J Biol Chem
; 295(35): 12485-12497, 2020 08 28.
Artigo
Inglês
| MEDLINE | ID: mdl-32665401
7.
Systems Analysis of the 22q11.2 Microdeletion Syndrome Converges on a Mitochondrial Interactome Necessary for Synapse Function and Behavior.
J Neurosci
; 39(18): 3561-3581, 2019 05 01.
Artigo
Inglês
| MEDLINE | ID: mdl-30833507
8.
Regulation of mitochondrial fragmentation in microvascular endothelial cells isolated from the SU5416/hypoxia model of pulmonary arterial hypertension.
Am J Physiol Lung Cell Mol Physiol
; 317(5): L639-L652, 2019 11 01.
Artigo
Inglês
| MEDLINE | ID: mdl-31461316
9.
Defining functional classes of Barth syndrome mutation in humans.
Hum Mol Genet
; 25(9): 1754-70, 2016 05 01.
Artigo
Inglês
| MEDLINE | ID: mdl-26908608
10.
Natural and Induced Mitochondrial Phosphate Carrier Loss: DIFFERENTIAL DEPENDENCE OF MITOCHONDRIAL METABOLISM AND DYNAMICS AND CELL SURVIVAL ON THE EXTENT OF DEPLETION.
J Biol Chem
; 291(50): 26126-26137, 2016 Dec 09.
Artigo
Inglês
| MEDLINE | ID: mdl-27780865
11.
Specific degradation of phosphatidylglycerol is necessary for proper mitochondrial morphology and function.
Biochim Biophys Acta
; 1857(1): 34-45, 2016 Jan.
Artigo
Inglês
| MEDLINE | ID: mdl-26482708
12.
The complexity of cardiolipin in health and disease.
Trends Biochem Sci
; 37(1): 32-41, 2012 Jan.
Artigo
Inglês
| MEDLINE | ID: mdl-22014644
13.
Phosphatidylserine decarboxylase 1 autocatalysis and function does not require a mitochondrial-specific factor.
J Biol Chem
; 290(20): 12744-52, 2015 May 15.
Artigo
Inglês
| MEDLINE | ID: mdl-25829489
14.
Unremodeled and remodeled cardiolipin are functionally indistinguishable in yeast.
J Biol Chem
; 289(3): 1768-78, 2014 Jan 17.
Artigo
Inglês
| MEDLINE | ID: mdl-24285538
15.
Seven functional classes of Barth syndrome mutation.
Hum Mol Genet
; 22(3): 483-92, 2013 Feb 01.
Artigo
Inglês
| MEDLINE | ID: mdl-23100323
16.
Acyl-CoA thioesterase-2 facilitates mitochondrial fatty acid oxidation in the liver.
J Lipid Res
; 55(12): 2458-70, 2014 Dec.
Artigo
Inglês
| MEDLINE | ID: mdl-25114170
17.
The Taz1p transacylase is imported and sorted into the outer mitochondrial membrane via a membrane anchor domain.
Eukaryot Cell
; 12(12): 1600-8, 2013 Dec.
Artigo
Inglês
| MEDLINE | ID: mdl-24078306
18.
Stem cell models of TAFAZZIN deficiency reveal novel tissue-specific pathologies in Barth Syndrome.
bioRxiv
; 2024 Apr 29.
Artigo
Inglês
| MEDLINE | ID: mdl-38746168
19.
Phosphatidylethanolamine biosynthesis in mitochondria: phosphatidylserine (PS) trafficking is independent of a PS decarboxylase and intermembrane space proteins UPS1P and UPS2P.
J Biol Chem
; 287(52): 43961-71, 2012 Dec 21.
Artigo
Inglês
| MEDLINE | ID: mdl-23124206
20.
Role for two conserved intermembrane space proteins, Ups1p and Ups2p, [corrected] in intra-mitochondrial phospholipid trafficking.
J Biol Chem
; 287(19): 15205-18, 2012 May 04.
Artigo
Inglês
| MEDLINE | ID: mdl-22403410