RESUMO
A female infant born at 41+6 weeks via emergency caesarean section due to failure to progress and maternal sepsis was found to have a small fibrous band connecting the upper and lower eyelids of the right eye. This was diagnosed as ankyloblepharon filiforme adnatum. The child was investigated for multisystemic malformations by the paediatric department, but none were found, and the partially fused right eyelid was dissected using microsurgical scissors to allow full opening of the eye. We summarise the management of a rare oculoplastic disorder.
Assuntos
Fenda Labial/cirurgia , Fissura Palatina/cirurgia , Anormalidades do Olho/cirurgia , Pálpebras/cirurgia , Anestésicos Locais/uso terapêutico , Fenda Labial/diagnóstico , Fissura Palatina/diagnóstico , Anormalidades do Olho/diagnóstico , Pálpebras/anormalidades , Feminino , Humanos , Recém-Nascido , Unidades de Terapia Intensiva Neonatal , Lidocaína/uso terapêutico , Procedimentos Cirúrgicos Oftalmológicos/métodos , Resultado do TratamentoRESUMO
We describe the importance of collaboration between multiple surgical specialties in managing a complex case of sight-threatening severe proptosis in a young woman with type 2 neurofibromatosis (NF2) complicated by pre-existing contralateral blindness. Trans-nasal and lateral orbital surgical approaches were aided by stereotactic navigation to debulk a large frontal/sphenoid wing meningioma, which had been exerting pressure onto the right globe and optic nerve. The patient made an excellent postoperative recovery along with preserved residual visual acuity, normal neurology and a good aesthetic outcome.