RESUMO
Micropapillary transitional cell carcinoma is a rare (incidence of 0.7%) and highly aggressive variant of bladder carcinoma. Morphologically, it is characterized by small tight clusters of neoplastic cell floating in clear spaces resembling lymphatic channels. Its usual presentation is like a high grade and stage carcinoma and most often is associated with a variable component of conventional carcinoma or other variants. The usual sites of bladder cancer metastases are the lymph nodes, lungs, bone and liver. Soft tissues metastases from transitional cell carcinoma of the bladder occur infrequently. We report the cases of a 77-year-old man presenting with an abdominal soft tissue mass a six years after local excision of a micropapillary bladder carcinoma.
Assuntos
Parede Abdominal , Carcinoma de Células de Transição/secundário , Neoplasias de Tecidos Moles/secundário , Neoplasias da Bexiga Urinária/patologia , Idoso , Humanos , MasculinoRESUMO
We report the case of a 37-year-old man with infertility caused by bilateral testicular masses secondary to congenital adrenal hyperplasia (21-hydroxylase deficiency). Testicular biopsy was done and its was initially interpreted as Leydig cell tumor but after clinical information was histologically reclassified as tumor of the adrenogenital syndrome. The differential diagnosis with Leydig cell tumor is discussed and it must be established through the clinical, biochemical, radiological and pathological features.
Assuntos
Glândulas Suprarrenais , Hiperplasia Suprarrenal Congênita/complicações , Coristoma/complicações , Infertilidade Masculina/etiologia , Doenças Testiculares/complicações , 17-alfa-Hidroxiprogesterona/sangue , Hiperplasia Suprarrenal Congênita/sangue , Hormônio Adrenocorticotrópico/sangue , Adulto , Biópsia , Coristoma/diagnóstico , Coristoma/diagnóstico por imagem , Coristoma/patologia , Diagnóstico Diferencial , Erros de Diagnóstico , Humanos , Hidrocortisona/sangue , Tumor de Células de Leydig/diagnóstico , Imageamento por Ressonância Magnética , Masculino , Esteroide 21-Hidroxilase/genética , Esteroide 21-Hidroxilase/metabolismo , Doenças Testiculares/diagnóstico , Doenças Testiculares/diagnóstico por imagem , Doenças Testiculares/patologia , Neoplasias Testiculares/diagnóstico , UltrassonografiaRESUMO
El carcinoma micropapilar es una variante infrecuente de carcinoma vesical (incidencia del 0.7%) con comportamiento clínico agresivo. Histológicamente está constituido por nidos pequeños de células uroteliales dispuestas en lagunas que simulan invasión vascular y se suelen asociar a estadios clínicos avanzados y alto grado histológico. Estos tumores generalmente se asocian a otras variantes histológicas de carcinoma transicional. Los tumores de vejiga suelen metastatizar a ganglios linfáticos, pulmón, hueso e hígado, pero son excepcionales las metástasis a partes blandas. Presentamos el caso de un varón de 77 años que presentó una masa metástasica en partes blandas de pared abdominal a los 6 años de realizarle resección de un carcinoma transicional variante micropapilar de vejiga
Micropapillary transitional cell carcinoma is a rare (incidence of 0.7%) and highly aggressive variant of bladder carcinoma. Morphologically, it is characterized by small tight clusters of neoplastic cell floating in clear spaces resembling lymphatic channels. Its usual presentation is like a high grade and stage carcinoma and most often is associated with a variable component of conventional carcinoma or other variants. The usual sites of bladder cancer metastases are the lymph nodes, lungs, bone and liver. Soft tissues metastases from transitional cell carcinoma of the bladder occur infrequently. We report the cases of a 77-year-old man presenting with an abdominal soft tissue mass a six years after local excision of a micropapillary bladder carcinoma
Assuntos
Masculino , Idoso , Humanos , Carcinoma de Células de Transição/patologia , Carcinoma Papilar/patologia , Neoplasias de Tecidos Moles/secundário , Neoplasias da Bexiga Urinária/patologia , Neoplasias de Tecidos Moles/diagnóstico , Neoplasias de Tecidos Moles/terapiaRESUMO
Presentamos un caso de azoospermia secretora y masas testiculares bilaterales secundarias a hiperplasia adrenal congénita por déficit de 21-hidroxilasa en un varón de 37 años. La biopsia testicular fue informada como tumor de células de Leydig, pero se consideró el diagnóstico después de la información clínica, siendo el diagnóstico final de hiperplasia de restos adrenales en el testículo. Comentamos el diagnóstico diferencial con el tumor de células de Leydig insistiedo en la necesidad de diagnosticar esta lesión con una adecuada correlación clínica, analítica, radiológica e histológica (AU)
We report the case of a 37-year-old man with infertility caused by bilateral testicular masses secondary to congenital adrenal hyperplasia (21-hydroxylase deficiency). Testicular biopsy was done and its was initially interpreted as Leydig cell tumor but after clinical information was histologically reclassified as tumor of the adrenogenital syndrome. The differential diagnosis with Leydig cell tumor is discussed and it must be established through the clinical, biochemical, radiological and pathological features (AU)