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1.
Arch Dis Child ; 96(4): 398-406, 2011 Apr.
Artigo em Inglês | MEDLINE | ID: mdl-20371581

RESUMO

The objective of this review was to examine disease-specific functioning (ie, faecal functioning and disease-related psychosocial problems) and quality of life (QoL)in patients with anorectal malformations (ARMs) or Hirschsprung's disease across different developmental stages. A search on PubMed yielded 22 eligible studies which were analysed. Patients with ARM or Hirschsprung's disease report slightly more QoL problems than comparison groups. As compared with adolescents, children reported better QoL but worse disease-specific functioning. Relationships between disease-specific functioning and QoL remain unclear. Therefore, to disentangle the complex relationship between the faecal functioning of these patients and their QoL through childhood, adolescence and adulthood, longitudinal studies should examine disease-specific functioning with validated QoL questionnaires that include age-specific versions.


Assuntos
Doença de Hirschsprung/reabilitação , Qualidade de Vida , Adolescente , Fatores Etários , Malformações Anorretais , Anus Imperfurado/complicações , Anus Imperfurado/fisiopatologia , Anus Imperfurado/reabilitação , Criança , Pré-Escolar , Constipação Intestinal/etiologia , Incontinência Fecal/etiologia , Feminino , Doença de Hirschsprung/complicações , Doença de Hirschsprung/fisiopatologia , Humanos , Lactente , Masculino
17.
JAMA ; 282(4): 378, 1999 Jul 28.
Artigo em Inglês | MEDLINE | ID: mdl-10432036
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