RESUMO
Aortic aneurysms in childhood are rare disease entities and are usually seen in patients with genetic connective tissue disorders such as Marfans, Ehler-Danlos, and Loeys-Dietz syndrome (LDS). Patients affected with LDS present early in life and have a rapid disease progression. We report a case of repair of an ascending and aortic arch aneurysm in an infant with Loeys-Dietz syndrome.
Assuntos
Aorta Torácica/cirurgia , Aorta/cirurgia , Aneurisma Aórtico/cirurgia , Implante de Prótese Vascular/métodos , Síndrome de Loeys-Dietz/complicações , Progressão da Doença , Humanos , Lactente , Masculino , Resultado do TratamentoRESUMO
Congenital heart diseases are most common anomalies associated with tracheoesophageal fistula (TEF) and oesophageal atresia (EA). The physiology and anatomy of heart disease is major determinant factor influencing outcome in patients with TEF/EA. We present a successfully treated case of complex congenital heart anomaly of interrupted aortic arch (IAA) with aortopulmonary window (APW) with TEF/EA.