Detalhe da pesquisa
1.
Improvement in Lung Clearance Index and Chest Computed Tomography Scores with Elexacaftor/Tezacaftor/Ivacaftor Treatment in People with Cystic Fibrosis Aged 12 Years and Older - The RECOVER Trial.
Am J Respir Crit Care Med
; 208(9): 917-929, 2023 11 01.
Artigo
Inglês
| MEDLINE | ID: mdl-37703083
2.
Long-Term Safety and Efficacy of Elexacaftor/Tezacaftor/Ivacaftor in Children Aged ⩾6 Years with Cystic Fibrosis and at Least One F508del Allele: A Phase 3, Open-Label Clinical Trial.
Am J Respir Crit Care Med
; 208(1): 68-78, 2023 07 01.
Artigo
Inglês
| MEDLINE | ID: mdl-37154609
3.
The clinical impact of Lumacaftor-Ivacaftor on structural lung disease and lung function in children aged 6-11 with cystic fibrosis in a real-world setting.
Respir Res
; 24(1): 199, 2023 Aug 11.
Artigo
Inglês
| MEDLINE | ID: mdl-37568199
4.
A Phase 3 Open-Label Study of Elexacaftor/Tezacaftor/Ivacaftor in Children 6 through 11 Years of Age with Cystic Fibrosis and at Least One F508del Allele.
Am J Respir Crit Care Med
; 203(12): 1522-1532, 2021 06 15.
Artigo
Inglês
| MEDLINE | ID: mdl-33734030
5.
Role of extracellular vesicles in chronic lung disease.
Thorax
; 76(10): 1047-1056, 2021 10.
Artigo
Inglês
| MEDLINE | ID: mdl-33712504
6.
Precise Targeting of miRNA Sites Restores CFTR Activity in CF Bronchial Epithelial Cells.
Mol Ther
; 28(4): 1190-1199, 2020 04 08.
Artigo
Inglês
| MEDLINE | ID: mdl-32059764
7.
Increased extracellular vesicles mediate inflammatory signalling in cystic fibrosis.
Thorax
; 75(6): 449-458, 2020 06.
Artigo
Inglês
| MEDLINE | ID: mdl-32265339
8.
Repeatability of transient elastography in children.
Pediatr Res
; 88(4): 587-592, 2020 10.
Artigo
Inglês
| MEDLINE | ID: mdl-32357363
9.
Reply to Dournes and Benlala: Hierarchical Computed Tomography Scoring Systems Cannot Discriminate Between Reversible Bronchiectasis and Mucus Plugs.
Am J Respir Crit Care Med
; 209(8): 1039-1040, 2024 Apr 15.
Artigo
Inglês
| MEDLINE | ID: mdl-38354409
10.
Anaerobic bacteria cultured from cystic fibrosis airways correlate to milder disease: a multisite study.
Eur Respir J
; 52(1)2018 07.
Artigo
Inglês
| MEDLINE | ID: mdl-29946004
11.
Apples to apples? Comparative analyses of national CF registries.
Thorax
; 77(2): 112-113, 2022 02.
Artigo
Inglês
| MEDLINE | ID: mdl-34413164
12.
Transient elastography lacks precision in children.
Pediatr Res
; 92(1): 2, 2022 07.
Artigo
Inglês
| MEDLINE | ID: mdl-34465879
13.
Performance Characteristics, Intra- and Inter-Operator Agreement of Transient Elastography in Pediatric Nonalcoholic Fatty Liver Disease.
J Pediatr Gastroenterol Nutr
; 74(1): e18-e19, 2022 01 01.
Artigo
Inglês
| MEDLINE | ID: mdl-34321425
14.
Ivacaftor and Airway Inflammation in Preschool Children with Cystic Fibrosis.
Am J Respir Crit Care Med
; 204(5): 605-608, 2021 09 01.
Artigo
Inglês
| MEDLINE | ID: mdl-34077699
15.
Lipoxin A4 prevents tight junction disruption and delays the colonization of cystic fibrosis bronchial epithelial cells by Pseudomonas aeruginosa.
Am J Physiol Lung Cell Mol Physiol
; 310(11): L1053-61, 2016 06 01.
Artigo
Inglês
| MEDLINE | ID: mdl-27084849
16.
A functional variant of elafin with improved anti-inflammatory activity for pulmonary inflammation.
Mol Ther
; 23(1): 24-31, 2015 Jan.
Artigo
Inglês
| MEDLINE | ID: mdl-25189740
17.
Lower Airway Infection in Preschool Children with Cystic Fibrosis: An International Comparison.
Am J Respir Crit Care Med
; 201(6): 748-750, 2020 03 15.
Artigo
Inglês
| MEDLINE | ID: mdl-31769996
18.
The Role of Short-Chain Fatty Acids, Produced by Anaerobic Bacteria, in the Cystic Fibrosis Airway.
Am J Respir Crit Care Med
; 192(11): 1314-24, 2015 Dec 01.
Artigo
Inglês
| MEDLINE | ID: mdl-26266556
19.
Infantile pulmonary capillary haemangiomatosis: a lethal form of pulmonary hypertension.
Cardiol Young
; 26(4): 663-8, 2016 Apr.
Artigo
Inglês
| MEDLINE | ID: mdl-26175015
20.
Pattern recognition in acute wheeze.
Arch Dis Child Educ Pract Ed
; 106(1): 41-43, 2021 02.
Artigo
Inglês
| MEDLINE | ID: mdl-31255996