1.
Klin Padiatr
; 221(5): 308-9, 2009 Sep.
Artigo
em Inglês
| MEDLINE
| ID: mdl-19707994
RESUMO
This article is about a 9-year-old boy with known homozygous sickle cell disease who developed unilateral exophthalmia and eyelid swelling during a sickle cell crisis. The symptoms were due to a vaso-occlusive event in the orbital bones,known as orbital compression syndrome, which is a rare complication of sickle cell disease.