RESUMO
Congenital pulmonary airway malformation is a rare congenital abnormality of the lungs. It can manifest at any age and can lead to significant morbidity and mortality in infants and children. Some individuals with congenital lung malformations may present with respiratory symptoms right after birth, while others may remain asymptomatic for extended periods. We present a case of a 4-year-old female child who experienced recurrent chest infections. Imaging revealed type I congenital pulmonary airway malformation with an underlying infection. Despite the increased risks associated with surgery and the complexity of the disease, the patient underwent a posterolateral thoracotomy with resection of the right lower lobe. The patient achieved successful outcomes and was able to recover successfully following the surgery. This case study holds significance because several studies have focused on the timing and outcomes of surgical intervention in asymptomatic cases, there remains a lack of consensus regarding symptomatic patients and their outcomes after surgery. Keywords: case reports; neonates; pneumonia.