Detalhe da pesquisa
1.
The Cystic Fibrosis Transmembrane Conductance Regulator Potentiator Ivacaftor Augments Mucociliary Clearance Abrogating Cystic Fibrosis Transmembrane Conductance Regulator Inhibition by Cigarette Smoke.
Am J Respir Cell Mol Biol
; 56(1): 99-108, 2017 01.
Artigo
Inglês
| MEDLINE | ID: mdl-27585394
2.
Roflumilast reverses CFTR-mediated ion transport dysfunction in cigarette smoke-exposed mice.
Respir Res
; 18(1): 173, 2017 09 18.
Artigo
Inglês
| MEDLINE | ID: mdl-28923049
3.
Pediatric anaphylaxis in the operating room for anesthesia residents: a simulation study.
Paediatr Anaesth
; 27(2): 205-210, 2017 Feb.
Artigo
Inglês
| MEDLINE | ID: mdl-27957774
4.
Combination therapy with cystic fibrosis transmembrane conductance regulator modulators augment the airway functional microanatomy.
Am J Physiol Lung Cell Mol Physiol
; 310(10): L928-39, 2016 05 15.
Artigo
Inglês
| MEDLINE | ID: mdl-26968770
5.
Cigarette smoke induces systemic defects in cystic fibrosis transmembrane conductance regulator function.
Am J Respir Crit Care Med
; 188(11): 1321-30, 2013 Dec 01.
Artigo
Inglês
| MEDLINE | ID: mdl-24040746
6.
Platelet production and platelet destruction: assessing mechanisms of treatment effect in immune thrombocytopenia.
Blood
; 117(21): 5723-32, 2011 May 26.
Artigo
Inglês
| MEDLINE | ID: mdl-21389318
7.
Activation of the cystic fibrosis transmembrane conductance regulator by the flavonoid quercetin: potential use as a biomarker of ΔF508 cystic fibrosis transmembrane conductance regulator rescue.
Am J Respir Cell Mol Biol
; 43(5): 607-16, 2010 Nov.
Artigo
Inglês
| MEDLINE | ID: mdl-20042712
8.
Cystic fibrosis transmembrane conductance regulator protein repair as a therapeutic strategy in cystic fibrosis.
Curr Opin Pulm Med
; 16(6): 591-7, 2010 Nov.
Artigo
Inglês
| MEDLINE | ID: mdl-20829696
9.
A pharmacologic approach to acquired cystic fibrosis transmembrane conductance regulator dysfunction in smoking related lung disease.
PLoS One
; 7(6): e39809, 2012.
Artigo
Inglês
| MEDLINE | ID: mdl-22768130
10.
Epidemiology of spine trauma in an Irish regional trauma unit: a 4-year study.
Injury
; 39(4): 436-42, 2008 Apr.
Artigo
Inglês
| MEDLINE | ID: mdl-18321511