RESUMO
Aneurysms of the right atrium are rare in the paediatric population. We report a case of a foetal diagnosis of right atrial aneurysm with associated atrial tachycardia in foetal and postnatal life. Unique to our case are the findings of isolated pericardial effusion without hydrops fetalis and the development of aortic coarctation in postnatal life.
Assuntos
Coartação Aórtica/complicações , Coartação Aórtica/diagnóstico , Aneurisma Cardíaco/complicações , Aneurisma Cardíaco/diagnóstico , Disfunção Ventricular Esquerda/complicações , Disfunção Ventricular Esquerda/diagnóstico , Adulto , Coartação Aórtica/cirurgia , Feminino , Aneurisma Cardíaco/cirurgia , Humanos , Recém-Nascido , Gravidez , Ultrassonografia Pré-Natal , Disfunção Ventricular Esquerda/cirurgiaRESUMO
Right atrial aneurysm is a rare congenital heart condition defined as a dilation of the right atrium in the absence of an underlying cause [1]. The clinical presentation varies; most patients are asymptomatic, while others may experience arrhythmias or intracavitary thrombi [1, 2]. We report a case.
Assuntos
Apêndice Atrial , Aneurisma Cardíaco , Cardiopatias Congênitas , Humanos , Valor Preditivo dos Testes , Átrios do Coração/diagnóstico por imagem , Átrios do Coração/cirurgia , Aneurisma Cardíaco/diagnóstico por imagem , Aneurisma Cardíaco/cirurgia , Cardiopatias Congênitas/complicações , Cardiopatias Congênitas/diagnóstico por imagem , Cardiopatias Congênitas/cirurgiaRESUMO
Idiopathic dilatation of the right atrium is a rare malformation characterized by disproportionate growth of the right atrium in the absence of a cause that justifies it. We present the case of a patient with idiopathic dilatation of the right atrium diagnosed since fetal life.
La dilatación idiopática de la aurícula derecha (DIAD) es una malformación poco frecuente caracterizada por un crecimiento desproporcionado de la aurícula derecha en ausencia de una causa estructural o funcional que la justifique. Presentamos el caso de una paciente con DIAD con diagnóstico desde la etapa prenatal.
Assuntos
Átrios do Coração , Humanos , Dilatação , Átrios do Coração/anormalidades , Dilatação PatológicaRESUMO
Only a handful of congenital aneurysms of the right atrium have been reported in the literature. They are most commonly found in the third decade of life, and the differential diagnosis depends on the patient's age profile. They are associated with 5% risk of sudden cardiac death. Once diagnosed, they should be surgically removed even in the absence of symptoms.
Assuntos
Aneurisma Coronário/diagnóstico , Aneurisma Coronário/cirurgia , Idoso , Diagnóstico Diferencial , Átrios do Coração , Humanos , MasculinoRESUMO
Resumen La dilatación idiopática de la aurícula derecha (DIAD) es una malformación poco frecuente caracterizada por un crecimiento desproporcionado de la aurícula derecha en ausencia de una causa estructural o funcional que la justifique. Presentamos el caso de una paciente con DIAD con diagnóstico desde la etapa prenatal.
Abstract Idiopathic dilatation of the right atrium is a rare malformation characterized by disproportionate growth of the right atrium in the absence of a cause that justifies it. We present the case of a patient with idiopathic dilatation of the right atrium diagnosed since fetal life.
RESUMO
A 13-year-old boy presented with right atrial aneurysm and downward displacement of the anterior leaflet in the tricuspid valve into the right ventricle, without tricuspid valve regurgitation. Paroxysmal atrial flutter was caused by an abnormal electrical re-entry circuit, which could not be treated using catheter radiofrequency ablation. Therefore, the patient underwent surgical ablation and resection of the enlarged right atrial wall. The anterior leaflet of the tricuspid valve was plastered and displaced downward into the right ventricle, which resembled Ebstein's anomaly. Pathological evaluation revealed a thin wall that contained fibrous tissue with lipomatous degeneration and few muscular elements. No postoperative arrhythmia was observed.
Assuntos
Procedimentos Cirúrgicos Cardíacos/métodos , Anomalia de Ebstein/diagnóstico , Aneurisma Cardíaco/diagnóstico , Átrios do Coração , Adolescente , Ablação por Cateter/métodos , Anomalia de Ebstein/cirurgia , Ecocardiografia , Aneurisma Cardíaco/cirurgia , Humanos , Masculino , Tomografia Computadorizada por Raios XRESUMO
Giant right atrial aneurysm is a rare form of congenital heart disease with a wide spectrum of clinical presentation varying from asymptomatic patients to those with refractory atrial arrhythmias or severe airway obstruction. Diagnosis is often confused with other causes of right atrial dilation such as Ebstein disease. Because of its rare occurrence and variable clinical presentation, inconsistencies in medical and surgical management strategies exist between centers. We present five cases of giant right atrial aneurysm managed at our institution and discuss the clinical presentation, diagnostic challenges, and medical and surgical management.
Assuntos
Procedimentos Cirúrgicos Cardíacos , Aneurisma Cardíaco/diagnóstico , Aneurisma Cardíaco/cirurgia , Átrios do Coração/cirurgia , Cardiopatias Congênitas/diagnóstico , Cardiopatias Congênitas/cirurgia , Antiarrítmicos/uso terapêutico , Pré-Escolar , Diagnóstico Diferencial , Ecocardiografia Transesofagiana , Feminino , Aneurisma Cardíaco/embriologia , Aneurisma Cardíaco/fisiopatologia , Átrios do Coração/diagnóstico por imagem , Átrios do Coração/embriologia , Átrios do Coração/fisiopatologia , Cardiopatias Congênitas/embriologia , Cardiopatias Congênitas/fisiopatologia , Hemodinâmica , Humanos , Lactente , Recém-Nascido , Masculino , Valor Preditivo dos Testes , Fatores de Tempo , Resultado do Tratamento , Ultrassonografia Pré-Natal/métodosRESUMO
A 2-year-old boy with an incidental finding of massive cardiomegaly on a chest X-ray was diagnosed with a giant right atrial aneurysm upon further investigation with echocardiography. The patient underwent successful surgical reduction of the right atrium and closure of the patent foramen ovale to prevent thromboembolic complications and to lower the risk of atrial arrhythmias. The resected atrium had paper-thin walls and pathological features of interstitial fibrosis with endocardial thickening.
RESUMO
Right atrial aneurysm is a rare abnormality of unknown origin. Approximately half of patients with right atrial aneurysm show no symptoms. Right atrial aneurysm is usually detected by chance at any time between fetal and adult life and can be associated with atrial arrhythmia and systemic embolism. The diagnosis of right atrial aneurysm can be established with echocardiography, computed tomography (CT) or magnetic resonance imaging (MRI). Because of thromboembolic risk, aneurysmectomy is usually recommended. We review the case report of a 69-year-wold woman with right atrial appendiceal aneurysm, whose diagnosis was established by echocardiography and CT angiography.
RESUMO
Right atrial aneurysm is a rare abnormality of unknown origin. Approximately half of patients with right atrial aneurysm show no symptoms. Right atrial aneurysm is usually detected by chance at any time between fetal and adult life and can be associated with atrial arrhythmia and systemic embolism. The diagnosis of right atrial aneurysm can be established with echocardiography, computed tomography (CT) or magnetic resonance imaging (MRI). Because of thromboembolic risk, aneurysmectomy is usually recommended. We review the case report of a 69-year-wold woman with right atrial appendiceal aneurysm, whose diagnosis was established by echocardiography and CT angiography.
Assuntos
Adulto , Feminino , Humanos , Aneurisma , Angiografia , Arritmias Cardíacas , Ecocardiografia , Ecocardiografia Transesofagiana , Embolia , Imageamento por Ressonância MagnéticaRESUMO
A healthy 8 year old boy was referred to our hospital because of cardiomegaly on the chest X ray. No cardiac murmur was detected on chest examination and normal sinus rhythm was checked by electrocardiogram. The 2-D echocardiogram showed a huge dilated right atrium and a normal tricuspid valve and right ventricle. The findings of cardiac angiogram and MRI was compatible with the isolated giant right atrial aneurysm. For the prevention of atrial arrhythmia and thromboembolism, he underwent successful surgical reduction of the right atrium and cryoablation and the follow-up X ray showed no cardiomegaly.