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[Cutis marmorata telangiectatica congenita--case report]. / Cutis marmorata teleangiectatica congenita egy eset kapcsán.
Flach, Edina; Kellermayer, Richárd; Ertl, Tibor; Vida, Gabriella; Sárkány, Ilona; Funke, Simone; Gyarmati, Judit.
  • Flach E; Pécsi Tudományegyetem, Altalános Orvostudományi Kar, Szülészeti és Nogyógyászati Klinika, NIC, Pécs, Edesanyák útja 17., 7624. edina.flach@aok.pte.hu
Orv Hetil ; 148(36): 1717-20, 2007 Sep 09.
Article en Hu | MEDLINE | ID: mdl-17766224
ABSTRACT
Cutis marmorata telangiectatica congenita is a rare, usually congenital, localized or generalized cutaneous vascular abnormality characterized by a persistent cutis marmorata pattern, spider naevus-like telangiectasia and ulceration or atrophy of the involved skin, which frequently improves with age. Approximately 300 cases have been reported worldwide. The authors present a case of cutis marmorata telangiectatica congenita with typical clinical

findings:

phlebectasia of the scalp with ulceration, almost generalized persistent cutis marmorata, telangiectasia. No associated anomalies were detected. The relevant literature is also reviewed.
Asunto(s)
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Banco de datos: MEDLINE Asunto principal: Telangiectasia Hemorrágica Hereditaria / Recien Nacido Prematuro Límite: Humans / Newborn Idioma: Hu Año: 2007 Tipo del documento: Article
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Banco de datos: MEDLINE Asunto principal: Telangiectasia Hemorrágica Hereditaria / Recien Nacido Prematuro Límite: Humans / Newborn Idioma: Hu Año: 2007 Tipo del documento: Article