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Human-to-mouse prion-like propagation of mutant huntingtin protein.
Jeon, Iksoo; Cicchetti, Francesca; Cisbani, Giulia; Lee, Suji; Li, Endan; Bae, Jiwoo; Lee, Nayeon; Li, Ling; Im, Wooseok; Kim, Manho; Kim, Hyun Sook; Oh, Seung-Hun; Kim, Tae-Aug; Ko, Jung Jae; Aubé, Benoit; Oueslati, Abid; Kim, Yun Joong; Song, Jihwan.
  • Jeon I; CHA Stem Cell Institute, CHA University, Room 604, CHA Bio Complex, 335 Pangyo-ro, Bundang-gu, Seongnam-si, 13488, Gyeonggi-do, Republic of Korea.
  • Cicchetti F; Centre de recherche du CHU de Québec (CHUQ), Québec, QC, G1V 4G2, Canada.
  • Cisbani G; Département de Psychiatrie and Neurosciences, Université Laval, Québec, QC, G1V 0A6, Canada.
  • Lee S; Centre de recherche du CHU de Québec (CHUQ), Québec, QC, G1V 4G2, Canada.
  • Li E; CHA Stem Cell Institute, CHA University, Room 604, CHA Bio Complex, 335 Pangyo-ro, Bundang-gu, Seongnam-si, 13488, Gyeonggi-do, Republic of Korea.
  • Bae J; CHA Stem Cell Institute, CHA University, Room 604, CHA Bio Complex, 335 Pangyo-ro, Bundang-gu, Seongnam-si, 13488, Gyeonggi-do, Republic of Korea.
  • Lee N; CHA Stem Cell Institute, CHA University, Room 604, CHA Bio Complex, 335 Pangyo-ro, Bundang-gu, Seongnam-si, 13488, Gyeonggi-do, Republic of Korea.
  • Li L; CHA Stem Cell Institute, CHA University, Room 604, CHA Bio Complex, 335 Pangyo-ro, Bundang-gu, Seongnam-si, 13488, Gyeonggi-do, Republic of Korea.
  • Im W; CHA Stem Cell Institute, CHA University, Room 604, CHA Bio Complex, 335 Pangyo-ro, Bundang-gu, Seongnam-si, 13488, Gyeonggi-do, Republic of Korea.
  • Kim M; Department of Neurology, Seoul National University Hospital, Seoul, Korea.
  • Kim HS; Department of Neurology, Seoul National University Hospital, Seoul, Korea.
  • Oh SH; CHA Stem Cell Institute, CHA University, Room 604, CHA Bio Complex, 335 Pangyo-ro, Bundang-gu, Seongnam-si, 13488, Gyeonggi-do, Republic of Korea.
  • Kim TA; CHA Stem Cell Institute, CHA University, Room 604, CHA Bio Complex, 335 Pangyo-ro, Bundang-gu, Seongnam-si, 13488, Gyeonggi-do, Republic of Korea.
  • Ko JJ; CHA Stem Cell Institute, CHA University, Room 604, CHA Bio Complex, 335 Pangyo-ro, Bundang-gu, Seongnam-si, 13488, Gyeonggi-do, Republic of Korea.
  • Aubé B; CHA Stem Cell Institute, CHA University, Room 604, CHA Bio Complex, 335 Pangyo-ro, Bundang-gu, Seongnam-si, 13488, Gyeonggi-do, Republic of Korea.
  • Oueslati A; Centre de recherche du CHU de Québec (CHUQ), Québec, QC, G1V 4G2, Canada.
  • Kim YJ; Centre de recherche du CHU de Québec (CHUQ), Québec, QC, G1V 4G2, Canada.
  • Song J; Département de Médecine Moléculaire, Université Laval, Québec, QC, G1V 0A6, Canada.
Acta Neuropathol ; 132(4): 577-92, 2016 10.
Article en En | MEDLINE | ID: mdl-27221146

Texto completo: 1 Banco de datos: MEDLINE Asunto principal: Enfermedad de Huntington / Proteínas Mutantes / Células Madre Pluripotentes Inducidas / Proteína Huntingtina / Neuronas Tipo de estudio: Prognostic_studies Límite: Animals / Child / Humans / Male Idioma: En Año: 2016 Tipo del documento: Article

Texto completo: 1 Banco de datos: MEDLINE Asunto principal: Enfermedad de Huntington / Proteínas Mutantes / Células Madre Pluripotentes Inducidas / Proteína Huntingtina / Neuronas Tipo de estudio: Prognostic_studies Límite: Animals / Child / Humans / Male Idioma: En Año: 2016 Tipo del documento: Article