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Ammonium accumulation is a primary effect of 2-methylcitrate exposure in an in vitro model for brain damage in methylmalonic aciduria.
Cudré-Cung, Hong-Phuc; Zavadakova, Petra; do Vale-Pereira, Sónia; Remacle, Noémie; Henry, Hugues; Ivanisevic, Julijana; Tavel, Denise; Braissant, Olivier; Ballhausen, Diana.
  • Cudré-Cung HP; Center of Molecular Diseases, Lausanne University Hospital, Switzerland.
  • Zavadakova P; Center of Molecular Diseases, Lausanne University Hospital, Switzerland.
  • do Vale-Pereira S; Center of Molecular Diseases, Lausanne University Hospital, Switzerland.
  • Remacle N; Center of Molecular Diseases, Lausanne University Hospital, Switzerland.
  • Henry H; Biomedicine, Innovation & Development, Lausanne University Hospital, Switzerland.
  • Ivanisevic J; Metabolomics Research Platform, Faculty of Biology and Medicine, University of Lausanne, Switzerland.
  • Tavel D; Department of Physiology, Lausanne University, Switzerland.
  • Braissant O; Biomedicine, Lausanne University Hospital, Switzerland.
  • Ballhausen D; Center of Molecular Diseases, Lausanne University Hospital, Switzerland. Electronic address: diana.ballhausen@chuv.ch.
Mol Genet Metab ; 119(1-2): 57-67, 2016 09.
Article en En | MEDLINE | ID: mdl-27599447

Texto completo: 1 Banco de datos: MEDLINE Asunto principal: Lesiones Encefálicas / Citratos / Compuestos de Amonio / Errores Innatos del Metabolismo de los Aminoácidos Límite: Animals / Humans Idioma: En Año: 2016 Tipo del documento: Article

Texto completo: 1 Banco de datos: MEDLINE Asunto principal: Lesiones Encefálicas / Citratos / Compuestos de Amonio / Errores Innatos del Metabolismo de los Aminoácidos Límite: Animals / Humans Idioma: En Año: 2016 Tipo del documento: Article