Muscle weakness in respiratory and peripheral skeletal muscles in a mouse model for nebulin-based nemaline myopathy.

Joureau, Barbara; de Winter, Josine M; Stam, Kelly; Granzier, Henk; Ottenheijm, Coen A C

Joureau, Barbara; de Winter, Josine M; Stam, Kelly; Granzier, Henk; Ottenheijm, Coen A C.

Joureau B; Department of Physiology, VU University Medical Center Amsterdam, The Netherlands.
de Winter JM; Department of Physiology, VU University Medical Center Amsterdam, The Netherlands.
Stam K; Department of Physiology, VU University Medical Center Amsterdam, The Netherlands.
Granzier H; Department of Cellular and Molecular Medicine, University of Arizona, Tucson, AZ, USA.
Ottenheijm CA; Department of Physiology, VU University Medical Center Amsterdam, The Netherlands; Department of Cellular and Molecular Medicine, University of Arizona, Tucson, AZ, USA. Electronic address: c.ottenheijm@vumc.nl.

Neuromuscul Disord ; 27(1): 83-89, 2017 Jan.

Article en En | MEDLINE | ID: mdl-27890461

Asunto(s)

Fibras Musculares Esqueléticas; Proteínas Musculares/genética; Debilidad Muscular/fisiopatología; Músculo Esquelético/fisiopatología; Miopatías Nemalínicas/fisiopatología; Insuficiencia Respiratoria/fisiopatología; Animales; Diafragma/fisiopatología; Modelos Animales de Enfermedad; Ratones; Debilidad Muscular/genética; Miopatías Nemalínicas/genética; Insuficiencia Respiratoria/genética

Palabras clave

Diaphragm; Nebulin; Nemaline myopathy; Respiratory failure

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Texto completo: 1 Banco de datos: MEDLINE Asunto principal: Insuficiencia Respiratoria / Miopatías Nemalínicas / Músculo Esquelético / Fibras Musculares Esqueléticas / Debilidad Muscular / Proteínas Musculares Límite: Animals Idioma: En Año: 2017 Tipo del documento: Article

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