Chronic granulomatous disease as a risk factor for cutaneous lupus in childhood.
Dermatol Online J
; 23(3)2017 Mar 15.
Article
en En
| MEDLINE
| ID: mdl-28329526
ABSTRACT
Chronic granulomatous disease (CGD) is a primaryimmunodeficiency disorder that affects the phagocyticcells of the innate immune system. It is characterizedby recurrent or persistent infections with granulomaformation. Lupus-like lesions have been reported incarriers of CGD and less frequently, in patients withCGD. Immunological study in these patients areusually negative. We describe the case of an 8-yearoldboy with CGD who developed chronic and acutecutaneous lupus erythematous with angular cheilitis,oral ulcers, Raynaud phenomenon, and positiveserologies for antinuclear, anticentromere, and anti-Saccharomyces cerevisiae antibodies.
Search on Google
Banco de datos:
MEDLINE
Asunto principal:
Lupus Eritematoso Cutáneo
/
Dermatosis Facial
/
Dermatosis del Pie
/
Enfermedad Granulomatosa Crónica
Tipo de estudio:
Diagnostic_studies
/
Etiology_studies
/
Risk_factors_studies
Límite:
Child
/
Humans
/
Male
Idioma:
En
Año:
2017
Tipo del documento:
Article