Angiomatoid Fibrous Histiocytoma With Paraneoplastic Platelet Storage Pool Deficiency.
Pediatrics
; 141(3)2018 03.
Article
en En
| MEDLINE
| ID: mdl-29472492
ABSTRACT
Angiomatoid fibrous histiocytoma is a rare soft tissue tumor usually discovered in young individuals. This tumor is often mistaken for a hematoma and typically misdiagnosed. It is commonly found in the extremities and may be associated with a site of recent or previous trauma. Characteristic histology includes nodules of histiocytoid spindle cells with pseudoangiomatoid spaces, fibrous pseudocapsules, and lymphoid cuffing. We describe the case of an 8-year-old girl who presented after incision and drainage of a superficial thigh lesion and experienced subsequent chronic bleeding of her wound. Her initial presentation was concerning for an underlying bleeding disorder, and laboratory analysis uncovered a paraneoplastic platelet function disorder that resolved with therapy of the primary tumor.
Texto completo:
1
Banco de datos:
MEDLINE
Asunto principal:
Neoplasias de los Tejidos Blandos
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Deficiencia de Almacenamiento del Pool Plaquetario
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Histiocitoma Fibroso Maligno
Tipo de estudio:
Diagnostic_studies
Límite:
Child
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Female
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Humans
Idioma:
En
Año:
2018
Tipo del documento:
Article