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Developmental defects and aberrant accumulation of endogenous psychosine in oligodendrocytes in a murine model of Krabbe disease.
Inamura, Naoko; Kito, Momoko; Go, Shinji; Kishi, Soichiro; Hosokawa, Masanori; Asai, Kiyofumi; Takakura, Nobuyuki; Takebayashi, Hirohide; Matsuda, Junko; Enokido, Yasushi.
  • Inamura N; Department of Pathology, Institute for Developmental Research, Aichi Human Service Center, 713-8 Kamiya-cho, Kasugai, Aichi 480-0392, Japan.
  • Kito M; Department of Pathology, Institute for Developmental Research, Aichi Human Service Center, 713-8 Kamiya-cho, Kasugai, Aichi 480-0392, Japan; Department of Molecular Neurobiology, Nagoya City University School of Medicine, 1 Kawasumi, Mizuho-cho, Mizuho-ku Nagoya, Aichi 467-8601, Japan.
  • Go S; Department of Pathophysiology and Metabolism, Kawasaki Medical School, 577 Matsushima, Kurashiki, Okayama 701-0192, Japan.
  • Kishi S; Department of Pathology, Institute for Developmental Research, Aichi Human Service Center, 713-8 Kamiya-cho, Kasugai, Aichi 480-0392, Japan.
  • Hosokawa M; Department of Pathology, Institute for Developmental Research, Aichi Human Service Center, 713-8 Kamiya-cho, Kasugai, Aichi 480-0392, Japan.
  • Asai K; Department of Molecular Neurobiology, Nagoya City University School of Medicine, 1 Kawasumi, Mizuho-cho, Mizuho-ku Nagoya, Aichi 467-8601, Japan.
  • Takakura N; Department of Signal Transduction, Research Institute for Microbial Diseases, Osaka University, 3-1 Yamadaoka, Suita, Osaka 565-0871, Japan.
  • Takebayashi H; Division of Neurobiology and Anatomy, Graduate School of Medicine and Dental Science, Niigata University, 1-757 Asahimachi-dori, Chuo-ku, Niigata 951-8510, Japan.
  • Matsuda J; Department of Pathophysiology and Metabolism, Kawasaki Medical School, 577 Matsushima, Kurashiki, Okayama 701-0192, Japan.
  • Enokido Y; Department of Pathology, Institute for Developmental Research, Aichi Human Service Center, 713-8 Kamiya-cho, Kasugai, Aichi 480-0392, Japan. Electronic address: enokido@inst-hsc.jp.
Neurobiol Dis ; 120: 51-62, 2018 12.
Article en En | MEDLINE | ID: mdl-30176352

Texto completo: 1 Banco de datos: MEDLINE Asunto principal: Psicosina / Oligodendroglía / Modelos Animales de Enfermedad / Leucodistrofia de Células Globoides Límite: Animals Idioma: En Año: 2018 Tipo del documento: Article

Texto completo: 1 Banco de datos: MEDLINE Asunto principal: Psicosina / Oligodendroglía / Modelos Animales de Enfermedad / Leucodistrofia de Células Globoides Límite: Animals Idioma: En Año: 2018 Tipo del documento: Article