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Treatment of keratinocytes with 4-phenylbutyrate in epidermolysis bullosa: Lessons for therapies in keratin disorders.
Spörrer, Marina; Prochnicki, Ania; Tölle, Regine C; Nyström, Alexander; Esser, Philipp R; Homberg, Melanie; Athanasiou, Ioannis; Zingkou, Eleni; Schilling, Achim; Gerum, Richard; Thievessen, Ingo; Winter, Lilli; Bruckner-Tuderman, Leena; Fabry, Ben; Magin, Thomas M; Dengjel, Jörn; Schröder, Rolf; Kiritsi, Dimitra.
  • Spörrer M; Department of Physics, Friedrich-Alexander-University Erlangen-Nuremberg, Erlangen, Germany.
  • Prochnicki A; Institute of Neuropathology, Friedrich-Alexander-University Erlangen-Nuremberg, Erlangen, Germany.
  • Tölle RC; Department of Biology, University of Fribourg, Switzerland.
  • Nyström A; Department of Dermatology, Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany.
  • Esser PR; Department of Dermatology, Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany.
  • Homberg M; Institute of Biology and SIKT, University of Leipzig, Leipzig, Germany.
  • Athanasiou I; Department of Dermatology, Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany.
  • Zingkou E; Department of Dermatology, Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany.
  • Schilling A; Department of Physics, Friedrich-Alexander-University Erlangen-Nuremberg, Erlangen, Germany; Experimental Otolaryngology, ENT Hospital, Head and Neck Surgery, Friedrich-Alexander University Erlangen-Nuremberg, Erlangen, Germany.
  • Gerum R; Department of Physics, Friedrich-Alexander-University Erlangen-Nuremberg, Erlangen, Germany.
  • Thievessen I; Department of Physics, Friedrich-Alexander-University Erlangen-Nuremberg, Erlangen, Germany.
  • Winter L; Institute of Neuropathology, Friedrich-Alexander-University Erlangen-Nuremberg, Erlangen, Germany.
  • Bruckner-Tuderman L; Department of Dermatology, Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany.
  • Fabry B; Department of Physics, Friedrich-Alexander-University Erlangen-Nuremberg, Erlangen, Germany.
  • Magin TM; Institute of Biology and SIKT, University of Leipzig, Leipzig, Germany.
  • Dengjel J; Department of Biology, University of Fribourg, Switzerland; Department of Dermatology, Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany.
  • Schröder R; Institute of Neuropathology, Friedrich-Alexander-University Erlangen-Nuremberg, Erlangen, Germany.
  • Kiritsi D; Department of Dermatology, Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany. Electronic address: dimitra.kiritsi@uniklinik-freiburg.de.
EBioMedicine ; 44: 502-515, 2019 Jun.
Article en En | MEDLINE | ID: mdl-31078522

Texto completo: 1 Banco de datos: MEDLINE Asunto principal: Fenilbutiratos / Queratinocitos / Epidermólisis Ampollosa / Queratinas Tipo de estudio: Etiology_studies / Prognostic_studies Límite: Animals / Humans Idioma: En Año: 2019 Tipo del documento: Article

Texto completo: 1 Banco de datos: MEDLINE Asunto principal: Fenilbutiratos / Queratinocitos / Epidermólisis Ampollosa / Queratinas Tipo de estudio: Etiology_studies / Prognostic_studies Límite: Animals / Humans Idioma: En Año: 2019 Tipo del documento: Article