Basosquamous carcinoma and melanoma collision tumor in a child with xeroderma pigmentosum.
Pediatr Dermatol
; 37(2): 390-392, 2020 Mar.
Article
en En
| MEDLINE
| ID: mdl-31957124
ABSTRACT
Xeroderma pigmentosum (XP) is a rare autosomal recessive genodermatosis associated with hypersensitivity to ultraviolet radiation (UVR), being due to defects involving the nucleotide excision repair pathway. Patients with XP are prone to develop multiple cutaneous neoplasms including non-melanoma skin cancers and melanoma. Collision tumors in patients with XP have been reported in the literature including the following lesions, actinic keratosis, basal cell carcinoma, squamous cell carcinoma, and in situ melanoma. Herein, we present a rare collision tumor composed of melanoma and basosquamous carcinoma in a 13-year-old XP patient and describe the dermoscopic features.
Palabras clave
Texto completo:
1
Banco de datos:
MEDLINE
Asunto principal:
Neoplasias Cutáneas
/
Xerodermia Pigmentosa
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Neoplasias Faciales
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Carcinoma Basoescamoso
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Melanoma
Tipo de estudio:
Etiology_studies
Límite:
Adolescent
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Humans
/
Male
Idioma:
En
Año:
2020
Tipo del documento:
Article