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Effects of acute nutritional ketosis during exercise in adults with glycogen storage disease type IIIa are phenotype-specific: An investigator-initiated, randomized, crossover study.
Hoogeveen, Irene J; de Boer, Foekje; Boonstra, Willemijn F; van der Schaaf, Caroline J; Steuerwald, Ulrike; Sibeijn-Kuiper, Anita J; Vegter, Riemer J K; van der Hoeven, Johannes H; Heiner-Fokkema, M Rebecca; Clarke, Kieran C; Cox, Pete J; Derks, Terry G J; Jeneson, Jeroen A L.
  • Hoogeveen IJ; Section of Metabolic Diseases, Beatrix Children's Hospital, University of Groningen, University Medical Center of Groningen, Groningen, The Netherlands.
  • de Boer F; Section of Metabolic Diseases, Beatrix Children's Hospital, University of Groningen, University Medical Center of Groningen, Groningen, The Netherlands.
  • Boonstra WF; Section of Metabolic Diseases, Beatrix Children's Hospital, University of Groningen, University Medical Center of Groningen, Groningen, The Netherlands.
  • van der Schaaf CJ; Section of Metabolic Diseases, Beatrix Children's Hospital, University of Groningen, University Medical Center of Groningen, Groningen, The Netherlands.
  • Steuerwald U; National Hospital of the Faroe Islands, Medical Center, Tórshavn, Faroe Islands.
  • Sibeijn-Kuiper AJ; Neuroimaging Center, Department of Neuroscience, University Medical Center Groningen, Groningen, The Netherlands.
  • Vegter RJK; Center for Human Movement Sciences, University Medical Center Groningen, University of Groningen, Groningen, The Netherlands.
  • van der Hoeven JH; Department of Neurology, University Medical Centre Groningen, University of Groningen, Groningen, The Netherlands.
  • Heiner-Fokkema MR; Department of Laboratory Medicine, Laboratory of Metabolic Diseases, University Medical Center Groningen, University of Groningen, Groningen, The Netherlands.
  • Clarke KC; Department of Physiology, Anatomy and Genetics, University of Oxford, Oxford, UK.
  • Cox PJ; Department of Physiology, Anatomy and Genetics, University of Oxford, Oxford, UK.
  • Derks TGJ; Section of Metabolic Diseases, Beatrix Children's Hospital, University of Groningen, University Medical Center of Groningen, Groningen, The Netherlands.
  • Jeneson JAL; Neuroimaging Center, Department of Neuroscience, University Medical Center Groningen, Groningen, The Netherlands.
J Inherit Metab Dis ; 44(1): 226-239, 2021 01.
Article en En | MEDLINE | ID: mdl-33448466

Texto completo: 1 Banco de datos: MEDLINE Asunto principal: Bebidas / Ejercicio Físico / Enfermedad del Almacenamiento de Glucógeno Tipo III / Cetosis / Enfermedades Musculares Tipo de estudio: Clinical_trials Límite: Adult / Female / Humans / Male / Middle aged País como asunto: Europa Idioma: En Año: 2021 Tipo del documento: Article

Texto completo: 1 Banco de datos: MEDLINE Asunto principal: Bebidas / Ejercicio Físico / Enfermedad del Almacenamiento de Glucógeno Tipo III / Cetosis / Enfermedades Musculares Tipo de estudio: Clinical_trials Límite: Adult / Female / Humans / Male / Middle aged País como asunto: Europa Idioma: En Año: 2021 Tipo del documento: Article