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Atypical Presentation of Juvenile Hyaline Fibromatosis of Hands.
Dukan, Ruben; Petroni, Gautier; Bruneval, Patrick; Pannier, Stephanie; Masmejean, Emmanuel H.
  • Dukan R; Hand, Upper Limb, and Peripheral Nerve Surgery Service, Georges-Pompidou European Hospital, Paris, France. Electronic address: ruben.dukan@aphp.fr.
  • Petroni G; Hand, Upper Limb, and Peripheral Nerve Surgery Service, Georges-Pompidou European Hospital, Paris, France.
  • Bruneval P; Department of Pathology Anatomy, Georges-Pompidou European Hospital, Paris, France; Medical School, University of Paris, Paris, France.
  • Pannier S; Pediatric Orthopedic Department, Necker Enfants Malades, Paris, France; Medical School, University of Paris, Paris, France.
  • Masmejean EH; Hand, Upper Limb, and Peripheral Nerve Surgery Service, Georges-Pompidou European Hospital, Paris, France; Medical School, University of Paris, Paris, France; Clinique Blomet (Research Unit), Paris, France.
J Hand Surg Am ; 47(2): 195.e1-195.e5, 2022 02.
Article en En | MEDLINE | ID: mdl-33726934
ABSTRACT
Juvenile hyaline fibromatosis is a rare disorder characterized by an extracellular accumulation of hyaline deposit. In the extremities, lesions may remain quiescent or gradually increase in size, eventually resulting in skin ulceration. There is no curative treatment. Surgery may allow some recovery of function, but recurrence is possible. We report a case of juvenile hyaline fibromatosis in both hands of a 25-year-old man who required multiple surgical procedures to address problems with function, pain, and appearance.
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Texto completo: 1 Banco de datos: MEDLINE Asunto principal: Neoplasias Cutáneas / Síndrome de Fibromatosis Hialina / Fibroma Tipo de estudio: Diagnostic_studies Límite: Adult / Humans / Male Idioma: En Año: 2022 Tipo del documento: Article

Texto completo: 1 Banco de datos: MEDLINE Asunto principal: Neoplasias Cutáneas / Síndrome de Fibromatosis Hialina / Fibroma Tipo de estudio: Diagnostic_studies Límite: Adult / Humans / Male Idioma: En Año: 2022 Tipo del documento: Article