Early medical treatment is life saving in acute Budd-Chiari due to polycythemia vera.
Hepatogastroenterology
; 50(50): 512-4, 2003.
Article
em En
| MEDLINE
| ID: mdl-12749260
ABSTRACT
Here we describe two women with polycythemia vera presented with fulminant hepatic failure due to acute Budd-Chiari syndrome. Both had a history of severe abdominal pain and distention of short duration. Clinical and laboratory findings showed fulminant hepatic failure due to acute Budd-Chiari syndrome. Diagnosis was confirmed with abdominal ultrasonography and Doppler ultrasonography showing ascites, hepatomegaly, portal hypertension and total occlusion of hepatic veins. Complete blood count and other clinical findings were compatible with polycythemia vera in both patients. Patients were treated successfully with early administration of continuous heparin infusion, repeated phlebotomies and hydroxyurea. We emphasize here early diagnosis and effective treatment in such fulminant cases may be life saving.
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Base de dados:
MEDLINE
Assunto principal:
Policitemia Vera
/
Heparina
/
Síndrome de Budd-Chiari
/
Hidroxiureia
/
Anticoagulantes
Tipo de estudo:
Diagnostic_studies
/
Etiology_studies
/
Screening_studies
Limite:
Adult
/
Female
/
Humans
Idioma:
En
Ano de publicação:
2003
Tipo de documento:
Article