Cutaneous angiosarcoma in a patient with xeroderma pigmentosum.
Indian J Pathol Microbiol
; 51(4): 504-6, 2008.
Article
em En
| MEDLINE
| ID: mdl-19008576
ABSTRACT
Xeroderma pigmentosum (XP) is a rare, autosomal recessive disorder characterized by photosensitivity, cutaneous pigmentary changes, premature skin ageing and development of various cutaneous and internal malignancies at an early age as a result of a defect in nucleotide excision repair following ultraviolet light exposure. Cutaneous angiosarcomas are aggressive neoplasms that are rarely associated with XP. In this communication, we report the case of a 40-year-old male patient with XP who developed an angiosarcoma of the face and discuss the implications of this association in view of recent developments in this field.
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Base de dados:
MEDLINE
Assunto principal:
Neoplasias Cutâneas
/
Xeroderma Pigmentoso
/
Hemangiossarcoma
Limite:
Adult
/
Humans
/
Male
Idioma:
En
Ano de publicação:
2008
Tipo de documento:
Article