Phosphaturic mesenchymal tumor, mixed connective tissue variant, of the mandible: report of a case and review of the literature.
Oral Surg Oral Med Oral Pathol Oral Radiol Endod
; 108(6): 925-32, 2009 Dec.
Article
em En
| MEDLINE
| ID: mdl-19828339
ABSTRACT
Tumor-induced osteomalacia (TIO) is a rare paraneoplastic syndrome that results in renal phosphate wasting with hypophosphatemia. In most cases, the underlying cause of TIO is a small mesenchymal neoplasm that is often difficult to detect, resulting in delayed diagnosis. One such neoplasm is the phosphaturic mesenchymal tumor, mixed connective tissue variant (PMTMCT), an unusual entity with unique morphologic and biochemical features. Most of these tumors are found at appendicular sites with only rare cases reported in the jaws. We describe a PMTMCT involving the mandible in a patient with a protracted history of osteomalacia. A review of the current literature is provided with emphasis on the clinical and histologic features, etiopathogenesis, and management of PMTMCT in the setting of TIO.
Texto completo:
1
Base de dados:
MEDLINE
Assunto principal:
Osteomalacia
/
Síndromes Paraneoplásicas
/
Neoplasias Mandibulares
/
Mesenquimoma
/
Neoplasias de Tecido Conjuntivo
Tipo de estudo:
Etiology_studies
Limite:
Adult
/
Female
/
Humans
Idioma:
En
Ano de publicação:
2009
Tipo de documento:
Article