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Effects of ivacaftor in patients with cystic fibrosis who carry the G551D mutation and have severe lung disease.
Barry, Peter J; Plant, Barry J; Nair, Arjun; Bicknell, Stephen; Simmonds, Nicholas J; Bell, Nicholas J; Shafi, Nadia T; Daniels, Thomas; Shelmerdine, Susan; Felton, Imogen; Gunaratnam, Cedric; Jones, Andrew M; Horsley, Alex R.
Afiliação
  • Barry PJ; University Hospital of South Manchester NHS Foundation Trust, Manchester, England.
  • Plant BJ; University Hospital of South Manchester NHS Foundation Trust, Manchester, England; Royal College of Physicians of Ireland, Dublin, Ireland; Cork University Hospital, University College Cork, Cork, Ireland.
  • Nair A; Royal Brompton Hospital and Imperial College, London, England.
  • Bicknell S; Gartnavel General Hospital, Glasgow, Scotland.
  • Simmonds NJ; Royal Brompton Hospital and Imperial College, London, England.
  • Bell NJ; Bristol Adult Cystic Fibrosis Centre, Bristol, England.
  • Shafi NT; Papworth Hospital, Cambridge, England.
  • Daniels T; University Hospital Southampton, Southampton, England.
  • Shelmerdine S; Royal Brompton Hospital and Imperial College, London, England.
  • Felton I; Royal Brompton Hospital and Imperial College, London, England.
  • Gunaratnam C; Beaumont Hospital, Dublin, Ireland.
  • Jones AM; University Hospital of South Manchester NHS Foundation Trust, Manchester, England.
  • Horsley AR; University Hospital of South Manchester NHS Foundation Trust, Manchester, England; University of Manchester, Manchester Academic Health Science Centre, University Hospital of South Manchester NHS Foundation Trust, Manchester, England. Electronic address: alexander.horsley@manchester.ac.uk.
Chest ; 146(1): 152-158, 2014 Jul.
Article em En | MEDLINE | ID: mdl-24522694

Texto completo: 1 Base de dados: MEDLINE Assunto principal: DNA / Quinolonas / Regulador de Condutância Transmembrana em Fibrose Cística / Fibrose Cística / Aminofenóis / Pneumopatias / Mutação Tipo de estudo: Diagnostic_studies / Observational_studies / Prognostic_studies / Risk_factors_studies Limite: Adult / Female / Humans / Male Idioma: En Ano de publicação: 2014 Tipo de documento: Article

Texto completo: 1 Base de dados: MEDLINE Assunto principal: DNA / Quinolonas / Regulador de Condutância Transmembrana em Fibrose Cística / Fibrose Cística / Aminofenóis / Pneumopatias / Mutação Tipo de estudo: Diagnostic_studies / Observational_studies / Prognostic_studies / Risk_factors_studies Limite: Adult / Female / Humans / Male Idioma: En Ano de publicação: 2014 Tipo de documento: Article