Neonatal kaposiform hemangioendothelioma of the spleen associated with Kasabach-Merritt phenomenon.
J Pediatr Surg
; 51(6): 1047-50, 2016 Jun.
Article
em En
| MEDLINE
| ID: mdl-27342010
ABSTRACT
Kaposiform hemangioendothelioma is a rare locally aggressive vascular tumor that usually manifests during early childhood. Typically the lesion presents with skin, soft tissue and bone involvement and is characterized histologically by ill-defined nodularity and the presence of spindle cells with resemblance to Kaposi's sarcoma. We report a rare neonatal case of a splenic kaposiform hemangioendothelioma associated with Kasabach-Merritt phenomenon that was diagnosed with radiographic imaging. Because of the rapid onset of thrombocytopenia and anemia, the patient required urgent splenectomy with subsequent resolution of the blood dyscrasias.
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Texto completo:
1
Base de dados:
MEDLINE
Assunto principal:
Sarcoma de Kaposi
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Baço
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Neoplasias Esplênicas
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Síndrome de Kasabach-Merritt
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Hemangioendotelioma
Tipo de estudo:
Diagnostic_studies
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Risk_factors_studies
Limite:
Humans
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Male
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Newborn
Idioma:
En
Ano de publicação:
2016
Tipo de documento:
Article