A Rare Case of Primary Myelofibrosis in a 14-Year-Old Patient With Congenital Asplenia.
J Pediatr Hematol Oncol
; 39(4): e196-e198, 2017 05.
Article
em En
| MEDLINE
| ID: mdl-27403772
ABSTRACT
Primary myelofibrosis (PMF) is rarely diagnosed in children, and in most cases in children younger than 3 years old. Pediatric PMF generally follows a benign course and is usually managed supportively with blood transfusions and prophylactic antibiotics for infections. We present a case of a 17-year-old girl diagnosed with PMF at the age of 14 years. A computed tomography scan performed at the time of an appendectomy showed congenital asplenism. To our knowledge, this is only the third case of myelofibrosis and congenital asplenism to be reported in the literature. Whether asplenism contributed to the development of myelofibrosis is not known.
Texto completo:
1
Base de dados:
MEDLINE
Assunto principal:
Baço
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Mielofibrose Primária
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Síndromes de Imunodeficiência
Tipo de estudo:
Diagnostic_studies
Limite:
Adolescent
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Female
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Humans
Idioma:
En
Ano de publicação:
2017
Tipo de documento:
Article