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SBDS-Deficient Cells Have an Altered Homeostatic Equilibrium due to Translational Inefficiency Which Explains their Reduced Fitness and Provides a Logical Framework for Intervention.
Calamita, Piera; Miluzio, Annarita; Russo, Arianna; Pesce, Elisa; Ricciardi, Sara; Khanim, Farhat; Cheroni, Cristina; Alfieri, Roberta; Mancino, Marilena; Gorrini, Chiara; Rossetti, Grazisa; Peluso, Ivana; Pagani, Massimiliano; Medina, Diego L; Rommens, Johanna; Biffo, Stefano.
Afiliação
  • Calamita P; INGM, National Institute of Molecular Genetics, "Romeo ed Enrica Invernizzi", Milan, Italy.
  • Miluzio A; INGM, National Institute of Molecular Genetics, "Romeo ed Enrica Invernizzi", Milan, Italy.
  • Russo A; INGM, National Institute of Molecular Genetics, "Romeo ed Enrica Invernizzi", Milan, Italy.
  • Pesce E; DiSIT, University of Eastern Piedmont, Alessandria, Italy.
  • Ricciardi S; INGM, National Institute of Molecular Genetics, "Romeo ed Enrica Invernizzi", Milan, Italy.
  • Khanim F; INGM, National Institute of Molecular Genetics, "Romeo ed Enrica Invernizzi", Milan, Italy.
  • Cheroni C; School of Biosciences, University of Birmingham Edgbaston Birmingham, United Kingdom.
  • Alfieri R; INGM, National Institute of Molecular Genetics, "Romeo ed Enrica Invernizzi", Milan, Italy.
  • Mancino M; INGM, National Institute of Molecular Genetics, "Romeo ed Enrica Invernizzi", Milan, Italy.
  • Gorrini C; INGM, National Institute of Molecular Genetics, "Romeo ed Enrica Invernizzi", Milan, Italy.
  • Rossetti G; Campbell Family Institute for Breast Cancer Research, University Health Network, Toronto, Ontario, Canada.
  • Peluso I; Princess Margaret Cancer Centre, University Health Network, Toronto, Ontario, Canada.
  • Pagani M; INGM, National Institute of Molecular Genetics, "Romeo ed Enrica Invernizzi", Milan, Italy.
  • Medina DL; Telethon Institute of Genetics and Medicine (TIGEM)-Fondazione Telethon, Pozzuoli, Italy.
  • Rommens J; INGM, National Institute of Molecular Genetics, "Romeo ed Enrica Invernizzi", Milan, Italy.
  • Biffo S; Department of Medical Biotechnology and Translational Medicine, University of Milan, Milan, Italy.
PLoS Genet ; 13(1): e1006552, 2017 01.
Article em En | MEDLINE | ID: mdl-28056084

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Fenótipo / Proteínas / Subunidades Ribossômicas Maiores de Eucariotos / Homeostase Limite: Animals Idioma: En Ano de publicação: 2017 Tipo de documento: Article

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Fenótipo / Proteínas / Subunidades Ribossômicas Maiores de Eucariotos / Homeostase Limite: Animals Idioma: En Ano de publicação: 2017 Tipo de documento: Article