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Loss-of-function mutations in co-chaperone BAG3 destabilize small HSPs and cause cardiomyopathy.
Fang, Xi; Bogomolovas, Julius; Wu, Tongbin; Zhang, Wei; Liu, Canzhao; Veevers, Jennifer; Stroud, Matthew J; Zhang, Zhiyuan; Ma, Xiaolong; Mu, Yongxin; Lao, Dieu-Hung; Dalton, Nancy D; Gu, Yusu; Wang, Celine; Wang, Michael; Liang, Yan; Lange, Stephan; Ouyang, Kunfu; Peterson, Kirk L; Evans, Sylvia M; Chen, Ju.
Afiliação
  • Fang X; Department of Medicine, UCSD, La Jolla, California, USA.
  • Bogomolovas J; Department of Medicine, UCSD, La Jolla, California, USA.
  • Wu T; Department of Cognitive and Clinical Neuroscience, Central Institute of Mental Health, Medical Faculty Mannheim, Heidelberg University, Mannheim, Germany.
  • Zhang W; Department of Medicine, UCSD, La Jolla, California, USA.
  • Liu C; Department of Medicine, UCSD, La Jolla, California, USA.
  • Veevers J; Department of Medicine, UCSD, La Jolla, California, USA.
  • Stroud MJ; Department of Medicine, UCSD, La Jolla, California, USA.
  • Zhang Z; Department of Medicine, UCSD, La Jolla, California, USA.
  • Ma X; Department of Medicine, UCSD, La Jolla, California, USA.
  • Mu Y; Department of Cardiothoracic Surgery, The Second Xiangya Hospital, Central South University, Changsha, Hunan, China.
  • Lao DH; Department of Medicine, UCSD, La Jolla, California, USA.
  • Dalton ND; Department of Cardiothoracic Surgery, The Second Xiangya Hospital, Central South University, Changsha, Hunan, China.
  • Gu Y; Department of Medicine, UCSD, La Jolla, California, USA.
  • Wang C; Department of Medicine, UCSD, La Jolla, California, USA.
  • Wang M; Department of Medicine, UCSD, La Jolla, California, USA.
  • Liang Y; Department of Medicine, UCSD, La Jolla, California, USA.
  • Lange S; Department of Medicine, UCSD, La Jolla, California, USA.
  • Ouyang K; Department of Medicine, UCSD, La Jolla, California, USA.
  • Peterson KL; Department of Medicine, UCSD, La Jolla, California, USA.
  • Evans SM; Department of Medicine, UCSD, La Jolla, California, USA.
  • Chen J; Drug Discovery Center, Key Laboratory of Chemical Genomics, Peking University Shenzhen Graduate School, Shenzhen, China.
J Clin Invest ; 127(8): 3189-3200, 2017 Aug 01.
Article em En | MEDLINE | ID: mdl-28737513

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Proteínas Adaptadoras de Transdução de Sinal / Proteínas Reguladoras de Apoptose / Proteínas de Choque Térmico / Mutação / Cardiomiopatias Limite: Animals Idioma: En Ano de publicação: 2017 Tipo de documento: Article

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Proteínas Adaptadoras de Transdução de Sinal / Proteínas Reguladoras de Apoptose / Proteínas de Choque Térmico / Mutação / Cardiomiopatias Limite: Animals Idioma: En Ano de publicação: 2017 Tipo de documento: Article