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Early cerebellar deficits in mitochondrial biogenesis and respiratory chain complexes in the KIKO mouse model of Friedreich ataxia.
Lin, Hong; Magrane, Jordi; Rattelle, Amy; Stepanova, Anna; Galkin, Alexander; Clark, Elisia M; Dong, Yi Na; Halawani, Sarah M; Lynch, David R.
Afiliação
  • Lin H; Departments of Pediatrics and Neurology, Children's Hospital of Philadelphia, Philadelphia, PA 19104, USA.
  • Magrane J; Feil Family Brain and Mind Research Institute, Weill Cornell Medical College, New York, NY 10065, USA.
  • Rattelle A; Departments of Pediatrics and Neurology, Children's Hospital of Philadelphia, Philadelphia, PA 19104, USA.
  • Stepanova A; Feil Family Brain and Mind Research Institute, Weill Cornell Medical College, New York, NY 10065, USA.
  • Galkin A; Queen's University Belfast, School of Biological Sciences, Medical Biology Centre, 97 Lisburn Road, Belfast BT9 7BL, UK.
  • Clark EM; Feil Family Brain and Mind Research Institute, Weill Cornell Medical College, New York, NY 10065, USA.
  • Dong YN; Queen's University Belfast, School of Biological Sciences, Medical Biology Centre, 97 Lisburn Road, Belfast BT9 7BL, UK.
  • Halawani SM; Departments of Pediatrics and Neurology, Children's Hospital of Philadelphia, Philadelphia, PA 19104, USA.
  • Lynch DR; Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA 19104, USA.
Dis Model Mech ; 10(11): 1343-1352, 2017 11 01.
Article em En | MEDLINE | ID: mdl-29125827

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Biogênese de Organelas / Ataxia de Friedreich / Cerebelo Tipo de estudo: Prognostic_studies Limite: Animals Idioma: En Ano de publicação: 2017 Tipo de documento: Article

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Biogênese de Organelas / Ataxia de Friedreich / Cerebelo Tipo de estudo: Prognostic_studies Limite: Animals Idioma: En Ano de publicação: 2017 Tipo de documento: Article