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Th1-skewed profile and excessive production of proinflammatory cytokines in a NFKB1-deficient patient with CVID and severe gastrointestinal manifestations.
Dieli-Crimi, Romina; Martínez-Gallo, Mónica; Franco-Jarava, Clara; Antolin, Maria; Blasco, Laura; Paramonov, Ida; Semidey, Maria E; Álvarez Fernández, Antoni; Molero, Xavier; Velásquez, Julio; Martín-Nalda, Andrea; Pujol-Borrell, Ricardo; Colobran, Roger.
Afiliação
  • Dieli-Crimi R; Immunology Division, Hospital Universitari Vall d'Hebron (HUVH), Vall d'Hebron Research Institute (VHIR), Department of Cell Biology, Physiology and Immunology, Autonomous University of Barcelona (UAB), Barcelona, Catalonia, Spain; Jeffrey Model Foundation Excellence Center, Barcelona, Catalonia, Sp
  • Martínez-Gallo M; Immunology Division, Hospital Universitari Vall d'Hebron (HUVH), Vall d'Hebron Research Institute (VHIR), Department of Cell Biology, Physiology and Immunology, Autonomous University of Barcelona (UAB), Barcelona, Catalonia, Spain; Jeffrey Model Foundation Excellence Center, Barcelona, Catalonia, Sp
  • Franco-Jarava C; Immunology Division, Hospital Universitari Vall d'Hebron (HUVH), Vall d'Hebron Research Institute (VHIR), Department of Cell Biology, Physiology and Immunology, Autonomous University of Barcelona (UAB), Barcelona, Catalonia, Spain; Jeffrey Model Foundation Excellence Center, Barcelona, Catalonia, Sp
  • Antolin M; Area of Clinical and Molecular Genetics, Hospital Universitari Vall d'Hebron (HUVH), Barcelona, Catalonia, Spain.
  • Blasco L; Area of Clinical and Molecular Genetics, Hospital Universitari Vall d'Hebron (HUVH), Barcelona, Catalonia, Spain.
  • Paramonov I; Area of Clinical and Molecular Genetics, Hospital Universitari Vall d'Hebron (HUVH), Barcelona, Catalonia, Spain.
  • Semidey ME; Pathology Department, Hospital Universitari Vall d'Hebron (HUVH), Barcelona, Catalonia, Spain.
  • Álvarez Fernández A; Pneumology Department, Hospital Universitari Vall d'Hebron (HUVH), Barcelona, Catalonia, Spain.
  • Molero X; Exocrine Pancreas Research Unit, Department of Digestive Diseases, Hospital Universitari Vall d'Hebron (HUVH), Autonomous University of Barcelona (UAB), CiberEHD, Barcelona, Catalonia, Spain.
  • Velásquez J; Exocrine Pancreas Research Unit, Department of Digestive Diseases, Hospital Universitari Vall d'Hebron (HUVH), Autonomous University of Barcelona (UAB), CiberEHD, Barcelona, Catalonia, Spain.
  • Martín-Nalda A; Jeffrey Model Foundation Excellence Center, Barcelona, Catalonia, Spain; Pediatric Infectious Diseases and Immunodeficiencies Unit (UPIIP), Hospital Universitari Vall d'Hebron (HUVH), Vall d'Hebron Research Institute (VHIR), Universitat Autònoma de Barcelona (UAB), Barcelona, Catalonia, Spain.
  • Pujol-Borrell R; Immunology Division, Hospital Universitari Vall d'Hebron (HUVH), Vall d'Hebron Research Institute (VHIR), Department of Cell Biology, Physiology and Immunology, Autonomous University of Barcelona (UAB), Barcelona, Catalonia, Spain; Jeffrey Model Foundation Excellence Center, Barcelona, Catalonia, Sp
  • Colobran R; Immunology Division, Hospital Universitari Vall d'Hebron (HUVH), Vall d'Hebron Research Institute (VHIR), Department of Cell Biology, Physiology and Immunology, Autonomous University of Barcelona (UAB), Barcelona, Catalonia, Spain; Jeffrey Model Foundation Excellence Center, Barcelona, Catalonia, Sp
Clin Immunol ; 195: 49-58, 2018 10.
Article em En | MEDLINE | ID: mdl-30063981

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Linfócitos B / NF-kappa B / Deleção de Sequência / Imunodeficiência de Variável Comum / Células Th1 / Gastroenteropatias Tipo de estudo: Prognostic_studies Limite: Adolescent / Adult / Female / Humans / Male Idioma: En Ano de publicação: 2018 Tipo de documento: Article

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Linfócitos B / NF-kappa B / Deleção de Sequência / Imunodeficiência de Variável Comum / Células Th1 / Gastroenteropatias Tipo de estudo: Prognostic_studies Limite: Adolescent / Adult / Female / Humans / Male Idioma: En Ano de publicação: 2018 Tipo de documento: Article