Ductopenia and cirrhosis in a 32-year-old woman with progressive familial intrahepatic cholestasis type 3: A case report and review of the literature.

Tan, You-Wen; Ji, Hai-Lei; Lu, Zhong-Hua; Ge, Guo-Hong; Sun, Li; Zhou, Xin-Bei; Sheng, Jian-Hui; Gong, Yu-Hua

Tan, You-Wen; Ji, Hai-Lei; Lu, Zhong-Hua; Ge, Guo-Hong; Sun, Li; Zhou, Xin-Bei; Sheng, Jian-Hui; Gong, Yu-Hua.

Afiliação

Tan YW; Department of Hepatology, The Third Hospital of Zhenjiang Affiliated Jiangsu University, Zhenjiang 212003, Jiangsu Province, China. tyw915@sina.com.
Ji HL; Department of Hepatology, The Third Hospital of Zhenjiang Affiliated Jiangsu University, Zhenjiang 212003, Jiangsu Province, China.
Lu ZH; Department of Liver Disease, Wuxi No. 5 People's Hospital Affiliated to Jiangnan University, Wuxi 214000, Jiangsu Province, China.
Ge GH; Department of Hepatology, The Third Hospital of Zhenjiang Affiliated Jiangsu University, Zhenjiang 212003, Jiangsu Province, China.
Sun L; Department of Hepatology, The Third Hospital of Zhenjiang Affiliated Jiangsu University, Zhenjiang 212003, Jiangsu Province, China.
Zhou XB; Department of Hepatology, The Third Hospital of Zhenjiang Affiliated Jiangsu University, Zhenjiang 212003, Jiangsu Province, China.
Sheng JH; Department of Hepatology, The Third Hospital of Zhenjiang Affiliated Jiangsu University, Zhenjiang 212003, Jiangsu Province, China.
Gong YH; Department of Hepatology, The Third Hospital of Zhenjiang Affiliated Jiangsu University, Zhenjiang 212003, Jiangsu Province, China.

World J Gastroenterol ; 24(41): 4716-4720, 2018 Nov 07.

Article em En | MEDLINE | ID: mdl-30416319

Assuntos

Subfamília B de Transportador de Cassetes de Ligação de ATP/deficiência; Ductos Biliares Intra-Hepáticos/patologia; Colestase Intra-Hepática/diagnóstico; Cirrose Hepática/diagnóstico; Ácido Ursodesoxicólico/uso terapêutico; gama-Glutamiltransferase/sangue; Subfamília B de Transportador de Cassetes de Ligação de ATP/genética; Adulto; Biópsia; Colestase Intra-Hepática/tratamento farmacológico; Colestase Intra-Hepática/genética; Colestase Intra-Hepática/patologia; Análise Mutacional de DNA; Feminino; Testes Genéticos; Humanos; Fígado/patologia; Cirrose Hepática/genética; Cirrose Hepática/patologia

Palavras-chave

Case report; Cirrhosis; Progressive familial intrahepatic cholestasis type 3

Texto completo

Imprimir

XML

PubMed Links

Buscar no Google

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Ácido Ursodesoxicólico / Ductos Biliares Intra-Hepáticos / Colestase Intra-Hepática / Subfamília B de Transportador de Cassetes de Ligação de ATP / Gama-Glutamiltransferase / Cirrose Hepática Tipo de estudo: Prognostic_studies Limite: Adult / Female / Humans Idioma: En Ano de publicação: 2018 Tipo de documento: Article

Texto completo

Imprimir

XML

PubMed Links

Buscar no Google