Acute lung injury after plasma exchange in a patient with anti-MDA5 antibody-positive, rapidly progressive, interstitial lung diseaseï¼A case report.
Respir Med Case Rep
; 29: 101016, 2020.
Article
em En
| MEDLINE
| ID: mdl-32055439
ADAMTS, a disintegrin-like and metalloproteinase with thrombospondin type 1 motifs; ALI, acute lung injury; ANA, antinuclear antibody; ANCA, antineutrophil cytoplasmic antibody; ARS, anti-aminoacyl-tRNA sythetase; Acute lung injury; Anti-MDA5 antibody; CADM, Clinically amyopathic dermatomyositis; CK, creatine phosphokinase; CRP, C-reactive protein; Clinically amyopathic dermatomyositis; EF, Ejection Fraction; GGA, ground-glass attenuation; IVCY, intravenous cyclophosphamide; Interstitial pneumonia; PE, plasma exchange; Plasma exchange; RP-ILD, rapidly progressive interstitial lung disease; SP-D, surfactant protein D; TRALI, Transfusion-related acute lung injury; anti-MDA5 Ab, anti-melanoma differentiation-associated gene 5 antibody
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En
Ano de publicação:
2020
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Article