Ventricular Tachycardia in a Patient With Dilated Cardiomyopathy Caused by a Novel Mutation of Lamin A/C Gene: Insights From Features on Electroanatomic Mapping, Catheter Ablation and Tissue Pathology.
Heart Lung Circ
; 30(2): 310-317, 2021 Feb.
Article
em En
| MEDLINE
| ID: mdl-33032896
ABSTRACT
Lamin A/C (LMNA) cardiomyopathy forms an important and increasingly recognised group within the broad spectrum of non-ischaemic cardiomyopathies. LMNA cardiomyopathy typically presents with atrioventricular block followed by recurrent ventricular arrhythmias with a high tendency to progression to end stage heart failure. We present a case of recurrent ventricular tachycardia in a patient with dilated cardiomyopathy caused by a novel mutation of LMNA gene. Through electroanatomic mapping, catheter ablation and tissue pathology we provide detailed insights into this highly pathogenic inherited cardiomyopathy.
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Texto completo:
1
Base de dados:
MEDLINE
Assunto principal:
DNA
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Cardiomiopatia Dilatada
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Taquicardia Ventricular
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Ablação por Cateter
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Lamina Tipo A
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Mutação
Tipo de estudo:
Etiology_studies
Limite:
Humans
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Male
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Middle aged
Idioma:
En
Ano de publicação:
2021
Tipo de documento:
Article