Neuroendocrine Tumor of the Common Bile Duct Associated With von Hippel-Lindau Disease.

ABSTRACT

We report a case of a common bile duct neuroendocrine tumor discovered in a patient with von Hippel-Lindau disease to emphasize the importance of recognizing this unusual diagnosis. This case illustrates the importance of endoscopic evaluation and the potential diagnostic pitfalls which may impact its appropriate management the anatomic proximity of more common von Hippel-Lindau disease-related tumors, pathologic evaluation, and staging. Therefore, awareness of this rare diagnosis is important for appropriate treatment.