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Thymoma and thymic carcinoma in children and adolescents: The EXPeRT/PARTNER diagnostic and therapeutic recommendations.
Stachowicz-Stencel, Teresa; Synakiewicz, Anna; Cornet, Marianna; Ferrari, Andrea; Garassino, Marina; Masip, Jordi Remon; Julien, Rod; Virgone, Calogero; Schneider, Dominik T; Brecht, Ines B; Ben-Ami, Tal; Bien, Ewa; Reguerre, Yves; Godzinski, Jan; Bisogno, Gianni; Orbach, Daniel; Sarnacki, Sabine.
Afiliação
  • Stachowicz-Stencel T; Department of Pediatrics, Hematology and Oncology, Medical University, Gdansk, Poland.
  • Synakiewicz A; Department of Pediatrics, Hematology and Oncology, Medical University, Gdansk, Poland.
  • Cornet M; Department of Pediatric Surgery, Hôpital Necker-Enfants Malades, Université de Paris, Paris, France.
  • Ferrari A; Paediatric Oncology Unit, Fondazione IRCCS Istituto Nazionale dei Tumori, Milan, Italy.
  • Garassino M; Thoraco-Pulmonary Medical Oncology Unit, Medical Oncology and Hematology Department, Fondazione IRCCS Istituto Nazionale dei Tumori, Milan, Italy.
  • Masip JR; Department of Cancer Medicine, Gustave Roussy, Villejuif, France.
  • Julien R; Department of Pediatric Surgery, University of Caen Hospital, Caen, France.
  • Virgone C; Pediatric Surgery, Department of Women's and Children's Health, University of Padua, Padua, Italy.
  • Schneider DT; Clinic of Pediatrics, Dortmund Municipal Hospital, Dortmund, Germany.
  • Brecht IB; Pediatric Oncology and Hematology, Children's Hospital, Eberhard-Karls-Universitaet, Tuebingen, Germany.
  • Ben-Ami T; Pediatric Hematology Unit, Kaplan Medical Center, Rehovot, Israel.
  • Bien E; Department of Pediatrics, Hematology and Oncology, Medical University, Gdansk, Poland.
  • Reguerre Y; Department of Pediatric Hematology and Oncology, Félix Guyon University Hospital, Réunion Island, Saint-Denis, France.
  • Godzinski J; Department of Pediatric Surgery, Marciniak Hospital, Wroclaw, Poland.
  • Bisogno G; Department of Pediatric Traumatology and Emergency Medicine, Wroclaw Medical University, Wroclaw, Poland.
  • Orbach D; Hematology and Oncology Division, Department for Women's and Children's Health, Padua University, Padua, Italy.
  • Sarnacki S; SIREDO Oncology Center (Care, Innovation and Research for Children, Adolescents and Young Adults with Cancer), Institut Curie, PSL University, Paris, France.
Pediatr Blood Cancer ; 68 Suppl 4: e29042, 2021 06.
Article em En | MEDLINE | ID: mdl-33881200
ABSTRACT
Thymic tumors are epithelial tumors arising from the anterior mediastinum and constitute 0.2-1.5% of all adult malignancies but are exceptional in pediatric population. Thymic epithelial tumors (TETs) encompass a variety of histologic subtypes associated with different clinical outcomes. Due to its rarity in children, TETs' management requires a multidisciplinary approach. However, prognosis remains still poor, especially among patients with thymic carcinoma. This study presents the internationally recognized recommendations for the diagnosis and treatment of thymic tumors in children and adolescents, established by the European Cooperative Study Group for Pediatric Rare Tumors (EXPeRT) group within the EU-funded project Paediatric Rare Tumours Network - European Registry (PARTNER).
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Texto completo: 1 Base de dados: MEDLINE Assunto principal: Timoma / Neoplasias do Timo / Neoplasias Epiteliais e Glandulares Tipo de estudo: Diagnostic_studies / Guideline / Prognostic_studies Limite: Adolescent / Adult / Child / Humans Idioma: En Ano de publicação: 2021 Tipo de documento: Article

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Timoma / Neoplasias do Timo / Neoplasias Epiteliais e Glandulares Tipo de estudo: Diagnostic_studies / Guideline / Prognostic_studies Limite: Adolescent / Adult / Child / Humans Idioma: En Ano de publicação: 2021 Tipo de documento: Article