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Successful treatment of congenital systemic juvenile xanthogranulomatosis with pulmonary involvement.
Ataseven, Eda; Kizmazoglu, Deniz; Oniz, Haldun.
Afiliação
  • Ataseven E; Division of Pediatric Hematology and Oncology, Department of Pediatrics, Ege University School of Medicine, Izmir, Turkey.
  • Kizmazoglu D; Division of Pediatric Hematology and Oncology, Department of Pediatrics, Izmir Tepecik Training and Research Hospital, Izmir, Turkey.
  • Oniz H; Division of Pediatric Hematology and Oncology, Department of Pediatrics, Izmir Tepecik Training and Research Hospital, Izmir, Turkey.
Pediatr Dermatol ; 38(4): 892-894, 2021 Jul.
Article em En | MEDLINE | ID: mdl-33998710
Juvenile xanthogranuloma (JXG) is a common form of non-Langerhans cell histiocytosis, which usually presents with spontaneously regressing skin lesions. Systemic involvement is rare and mostly seen in patients with multiple skin nodules. It can spontaneously regress, but sometimes systemic involvement can cause life-threatening symptoms and can be fatal. Herein, we report a case of congenital systemic JXG with multiple skin nodules, soft tissue and pulmonary involvement. She was successfully treated with chemotherapy according to Langerhans cell histiocytosis treatment protocol IV of the Histiocyte Society (LCH-IV).
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Texto completo: 1 Base de dados: MEDLINE Assunto principal: Neoplasias Cutâneas / Histiocitose de Células não Langerhans / Histiocitose de Células de Langerhans / Xantogranuloma Juvenil Tipo de estudo: Diagnostic_studies / Guideline Limite: Female / Humans Idioma: En Ano de publicação: 2021 Tipo de documento: Article

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Neoplasias Cutâneas / Histiocitose de Células não Langerhans / Histiocitose de Células de Langerhans / Xantogranuloma Juvenil Tipo de estudo: Diagnostic_studies / Guideline Limite: Female / Humans Idioma: En Ano de publicação: 2021 Tipo de documento: Article