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Patient-specific iPSCs carrying an SFTPC mutation reveal the intrinsic alveolar epithelial dysfunction at the inception of interstitial lung disease.
Alysandratos, Konstantinos-Dionysios; Russo, Scott J; Petcherski, Anton; Taddeo, Evan P; Acín-Pérez, Rebeca; Villacorta-Martin, Carlos; Jean, J C; Mulugeta, Surafel; Rodriguez, Luis R; Blum, Benjamin C; Hekman, Ryan M; Hix, Olivia T; Minakin, Kasey; Vedaie, Marall; Kook, Seunghyi; Tilston-Lunel, Andrew M; Varelas, Xaralabos; Wambach, Jennifer A; Cole, F Sessions; Hamvas, Aaron; Young, Lisa R; Liesa, Marc; Emili, Andrew; Guttentag, Susan H; Shirihai, Orian S; Beers, Michael F; Kotton, Darrell N.
Afiliação
  • Alysandratos KD; Center for Regenerative Medicine, Boston University and Boston Medical Center, Boston, MA 02118, USA; The Pulmonary Center and Department of Medicine, Boston University School of Medicine, Boston, MA 02118, USA.
  • Russo SJ; Pulmonary, Allergy, and Critical Care Division, Department of Medicine, University of Pennsylvania Perelman School of Medicine, Philadelphia, PA 19104, USA; PENN-CHOP Lung Biology Institute, University of Pennsylvania Perelman School of Medicine, Philadelphia, PA 19104, USA.
  • Petcherski A; Departments of Medicine, Endocrinology and Molecular and Medical Pharmacology, David Geffen School of Medicine at UCLA, Los Angeles, CA 90095, USA.
  • Taddeo EP; Departments of Medicine, Endocrinology and Molecular and Medical Pharmacology, David Geffen School of Medicine at UCLA, Los Angeles, CA 90095, USA.
  • Acín-Pérez R; Departments of Medicine, Endocrinology and Molecular and Medical Pharmacology, David Geffen School of Medicine at UCLA, Los Angeles, CA 90095, USA.
  • Villacorta-Martin C; Center for Regenerative Medicine, Boston University and Boston Medical Center, Boston, MA 02118, USA.
  • Jean JC; Center for Regenerative Medicine, Boston University and Boston Medical Center, Boston, MA 02118, USA; The Pulmonary Center and Department of Medicine, Boston University School of Medicine, Boston, MA 02118, USA.
  • Mulugeta S; Pulmonary, Allergy, and Critical Care Division, Department of Medicine, University of Pennsylvania Perelman School of Medicine, Philadelphia, PA 19104, USA; PENN-CHOP Lung Biology Institute, University of Pennsylvania Perelman School of Medicine, Philadelphia, PA 19104, USA.
  • Rodriguez LR; Pulmonary, Allergy, and Critical Care Division, Department of Medicine, University of Pennsylvania Perelman School of Medicine, Philadelphia, PA 19104, USA; PENN-CHOP Lung Biology Institute, University of Pennsylvania Perelman School of Medicine, Philadelphia, PA 19104, USA.
  • Blum BC; Departments of Biology and Biochemistry, Boston University School of Medicine, Boston, MA 02118, USA.
  • Hekman RM; Departments of Biology and Biochemistry, Boston University School of Medicine, Boston, MA 02118, USA.
  • Hix OT; Center for Regenerative Medicine, Boston University and Boston Medical Center, Boston, MA 02118, USA.
  • Minakin K; Center for Regenerative Medicine, Boston University and Boston Medical Center, Boston, MA 02118, USA.
  • Vedaie M; Center for Regenerative Medicine, Boston University and Boston Medical Center, Boston, MA 02118, USA; The Pulmonary Center and Department of Medicine, Boston University School of Medicine, Boston, MA 02118, USA.
  • Kook S; Department of Pediatrics, Monroe Carell Jr. Children's Hospital, Vanderbilt University, Nashville, TN 37232, USA.
  • Tilston-Lunel AM; Departments of Biochemistry, Boston University School of Medicine, Boston, MA 02118, USA.
  • Varelas X; Departments of Biochemistry, Boston University School of Medicine, Boston, MA 02118, USA.
  • Wambach JA; Division of Newborn Medicine, Edward Mallinckrodt Department of Pediatrics, Washington University School of Medicine and St. Louis Children's Hospital, St. Louis, MO 63110, USA.
  • Cole FS; Division of Newborn Medicine, Edward Mallinckrodt Department of Pediatrics, Washington University School of Medicine and St. Louis Children's Hospital, St. Louis, MO 63110, USA.
  • Hamvas A; Department of Pediatrics, Northwestern University Feinberg School of Medicine, Chicago, IL 60611, USA.
  • Young LR; Division of Pulmonary and Sleep Medicine, Department of Pediatrics, Children's Hospital of Philadelphia, Philadelphia, PA 19104, USA.
  • Liesa M; Departments of Medicine, Endocrinology and Molecular and Medical Pharmacology, David Geffen School of Medicine at UCLA, Los Angeles, CA 90095, USA.
  • Emili A; Departments of Biology and Biochemistry, Boston University School of Medicine, Boston, MA 02118, USA.
  • Guttentag SH; Department of Pediatrics, Monroe Carell Jr. Children's Hospital, Vanderbilt University, Nashville, TN 37232, USA.
  • Shirihai OS; Departments of Medicine, Endocrinology and Molecular and Medical Pharmacology, David Geffen School of Medicine at UCLA, Los Angeles, CA 90095, USA.
  • Beers MF; Pulmonary, Allergy, and Critical Care Division, Department of Medicine, University of Pennsylvania Perelman School of Medicine, Philadelphia, PA 19104, USA; PENN-CHOP Lung Biology Institute, University of Pennsylvania Perelman School of Medicine, Philadelphia, PA 19104, USA. Electronic address: mfbe
  • Kotton DN; Center for Regenerative Medicine, Boston University and Boston Medical Center, Boston, MA 02118, USA; The Pulmonary Center and Department of Medicine, Boston University School of Medicine, Boston, MA 02118, USA. Electronic address: dkotton@bu.edu.
Cell Rep ; 36(9): 109636, 2021 08 31.
Article em En | MEDLINE | ID: mdl-34469722
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Texto completo: 1 Base de dados: MEDLINE Assunto principal: Doenças Pulmonares Intersticiais / Proteína C Associada a Surfactante Pulmonar / Células Epiteliais Alveolares / Células-Tronco Pluripotentes Induzidas Tipo de estudo: Prognostic_studies Limite: Animals / Humans Idioma: En Ano de publicação: 2021 Tipo de documento: Article
Texto completo
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XML
PubMed Links
Buscar no Google

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Doenças Pulmonares Intersticiais / Proteína C Associada a Surfactante Pulmonar / Células Epiteliais Alveolares / Células-Tronco Pluripotentes Induzidas Tipo de estudo: Prognostic_studies Limite: Animals / Humans Idioma: En Ano de publicação: 2021 Tipo de documento: Article