Uhl's Anomaly With Left Ventricular Noncompaction: Role of Multimodality Imaging in a Rare Association.
JACC Case Rep
; 3(12): 1463-1467, 2021 Sep 15.
Article
em En
| MEDLINE
| ID: mdl-34557694
ABSTRACT
Uhl's anomaly is a rare congenital heart disease characterized by partial or complete absence of the right ventricle myocardium. We report the first case, in a 21-year-old man, of Uhl's anomaly-associated left ventricular noncompaction. This association represents a unique clinical entity and has important implications for management strategies. (Level of Difficulty Intermediate.).
ARVD/C, arrhythmogenic right ventricular dysplasia or cardiomyopathy; ASD, atrial septal defect; EDP, end-diastolic pressure; EF, ejection fraction; LV, left ventricular; LVNC, left ventricular noncompaction; PVD, pulmonary vascular disease; RA, right atrial; RV, right ventricular; TCPC, total cavopulmonary connection; TV, tricuspid valve; Uhl's anomaly; atrial septal defect; cardiac magnetic resonance; congenital heart defect; left ventricle; left ventricular noncompaction; right ventricle
Texto completo:
1
Base de dados:
MEDLINE
Tipo de estudo:
Risk_factors_studies
Idioma:
En
Ano de publicação:
2021
Tipo de documento:
Article