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Modeling of lung phenotype of Hermansky-Pudlak syndrome type I using patient-specific iPSCs.
Suezawa, Takahiro; Kanagaki, Shuhei; Korogi, Yohei; Nakao, Kazuhisa; Hirai, Toyohiro; Murakami, Koji; Hagiwara, Masatoshi; Gotoh, Shimpei.
Afiliação
  • Suezawa T; Department of Drug Discovery for Lung Diseases, Graduate School of Medicine, Kyoto University, Yoshida Konoe-cho, Sakyo-ku, Kyoto, 606-8501, Japan.
  • Kanagaki S; Watarase Research Center, Kyorin Pharmaceutical Co. Ltd., Shimotsuga-gun, Tochigi, Japan.
  • Korogi Y; Watarase Research Center, Kyorin Pharmaceutical Co. Ltd., Shimotsuga-gun, Tochigi, Japan.
  • Nakao K; Department of Respiratory Medicine, Graduate School of Medicine, Kyoto University, Kyoto, Japan.
  • Hirai T; Watarase Research Center, Kyorin Pharmaceutical Co. Ltd., Shimotsuga-gun, Tochigi, Japan.
  • Murakami K; Department of Respiratory Medicine, Graduate School of Medicine, Kyoto University, Kyoto, Japan.
  • Hagiwara M; Watarase Research Center, Kyorin Pharmaceutical Co. Ltd., Shimotsuga-gun, Tochigi, Japan.
  • Gotoh S; Department of Anatomy and Developmental Biology, Graduate School of Medicine, Kyoto University, Kyoto, Japan.
Respir Res ; 22(1): 284, 2021 Nov 04.
Article em En | MEDLINE | ID: mdl-34736469

Texto completo: 1 Base de dados: MEDLINE Assunto principal: DNA / Síndrome de Hermanski-Pudlak / Proteômica / Células Epiteliais Alveolares / Proteínas de Membrana / Mutação Limite: Animals / Humans / Male Idioma: En Ano de publicação: 2021 Tipo de documento: Article

Texto completo: 1 Base de dados: MEDLINE Assunto principal: DNA / Síndrome de Hermanski-Pudlak / Proteômica / Células Epiteliais Alveolares / Proteínas de Membrana / Mutação Limite: Animals / Humans / Male Idioma: En Ano de publicação: 2021 Tipo de documento: Article