Malignant Peripheral Nerve Sheath Tumor Arising from Small Bowel Mesentery: an Extremely Rare Case with Review of Literature.
J Gastrointest Cancer
; 54(1): 259-263, 2023 Mar.
Article
em En
| MEDLINE
| ID: mdl-34796455
ABSTRACT
PURPOSE:
Malignant peripheral nerve sheath tumor (MPNST) of small bowel mesentery is a rare tumor. We report a rare case of MPNST of small bowel mesentery in a patient without neurofibromatosis (NF).METHODS:
A 50-year-old male, with no features suggestive of NF1, presented to us with complaints of pain abdomen. Contrast-enhanced computed tomography (CECT) of the abdomen revealed a mass in the infrarenal region. On laparotomy, mass was seen to be arising from the mesentery of the jejunum. En-bloc resection of the tumor was done, and histopathological examination was suggestive of malignant peripheral nerve sheath tumor of the small bowel mesentery.RESULT:
Patient received adjuvant external beam radiotherapy to a dose of 50.4 Gy to the tumor bed. The patient was planned for chemotherapy but absconded and later came with recurrence. The patient finally succumbed to disease.CONCLUSION:
Surgery is the mainstay of treatment. Adjuvant treatment should be based on histopathological report.Palavras-chave
Texto completo:
1
Base de dados:
MEDLINE
Assunto principal:
Neurofibromatose 1
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Neurofibrossarcoma
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Neoplasias de Bainha Neural
Limite:
Humans
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Male
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Middle aged
Idioma:
En
Ano de publicação:
2023
Tipo de documento:
Article