A Rare Case of Dandy-Walker Syndrome.

Oria, Mohammad Sharif; Rasib, Aziz Rahman; Pirzad, Ahmad Fawad; Wali Ibrahim Khel, Fahima; Ibrahim Khel, Mohammad Ismael; Wardak, Fazel Rahim.

Afiliação

Oria MS; Anesthesiology Department, Kabul University of Medical Sciences, Kabul, 1001, Afghanistan.
Rasib AR; Neuropsychiatry Department, Kabul University of Medical Sciences, Kabul, 1001, Afghanistan.
Pirzad AF; Neurosurgery Department, Kabul University of Medical Sciences, Kabul, 1001, Afghanistan.
Wali Ibrahim Khel F; Gynecology and Obstetrics Department, Malalai Maternity Hospital, Kabul, 1003, Afghanistan.
Ibrahim Khel MI; Anesthesiology Department, Kabul University of Medical Sciences, Kabul, 1001, Afghanistan.
Wardak FR; Microbiology Department, Kabul University of Medical Sciences, Kabul, 1001, Afghanistan.

Int Med Case Rep J ; 15: 55-59, 2022.

Article em En | MEDLINE | ID: mdl-35210871

ABSTRACT

Dandy-Walker syndrome (DWS) is a rare congenital malformation characterized by hypoplasia of the cerebellar vermis and its upward rotation and cystic enlargement of the fourth ventricle. The clinical manifestations include psychomotor retardation, ataxia and hydrocephalus. We report a case of 16-year-old female patient in Ali Abad Teaching Hospital who was suffering from unsteady gait, memory deterioration and urinary incontinence. A brain magnetic resonance imaging revealed enlarged cystic posterior fossa, dilated fourth ventricles and upward rotated cerebellar vermis which were indicating DWS. The patient prepared for planned surgical operation and a written informed consent was obtained from her parents for surgery and general anesthesia. A cystoperitoneal (CP) shunt was placed and then the patient transferred to recovery room. After recovery and hospital stay, the patient discharged with improved clinical symptoms.

Palavras-chave

Dandy Walker syndrome; hydrocephalus; intubation challenge

Texto completo: 1 Base de dados: MEDLINE Idioma: En Ano de publicação: 2022 Tipo de documento: Article