Thoracic insufficiency syndrome: Approaches to assessment and management.
Paediatr Respir Rev
; 44: 78-84, 2022 Dec.
Article
em En
| MEDLINE
| ID: mdl-35339395
ABSTRACT
Thoracic insufficiency syndrome (TIS) was described in 2003 as the inability of the thorax to support normal respiration or lung growth. TIS includes a broad and disparate group of typically degenerative thoracospinal conditions. Although TIS arises due to a heterogeneous group of disorders and thus its incidence is not well quantified, general approaches to management and treatment exist. Evolving imaging techniques and measurements of health-related quality of life augment tests of pulmonary function to quantify disease burden, longitudinally and pre- and post-intervention. Intervention is primarily via growth-sparing surgery, for which several device options exist, to preserve vertical growth prior to a definitive spinal fusion at skeletal maturity.
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Texto completo:
1
Base de dados:
MEDLINE
Assunto principal:
Insuficiência Respiratória
Limite:
Humans
Idioma:
En
Ano de publicação:
2022
Tipo de documento:
Article