Idiopathic Hypereosinophilic Syndrome Associated With Pulmonary Hypertension in an Infant.
J Pediatr Hematol Oncol
; 44(5): e881-e883, 2022 07 01.
Article
em En
| MEDLINE
| ID: mdl-35383694
ABSTRACT
Hypereosinophilic syndrome (HES) is a very rare disease during childhood. It involves the different organs like skin, gastrointestinal system, heart and lungs, besides pulmonary hypertension (PHT) is a very rare morbidity of HES that may cause life-threatening complications. PHT improves with the treatment of hypereosinophilia, without the need for pulmonary vasodilator therapy. Here, we present a case of PHT developed after recovery of pulmonary infiltration in an infant with idiopathic HES. We revealed that pulmonary pressure returned to normal range in parallel with the decrease in eosinophil count with steroid treatment.
Texto completo:
1
Base de dados:
MEDLINE
Assunto principal:
Síndrome Hipereosinofílica
/
Hipertensão Pulmonar
Tipo de estudo:
Etiology_studies
/
Risk_factors_studies
Limite:
Humans
/
Infant
Idioma:
En
Ano de publicação:
2022
Tipo de documento:
Article