Selected severe „haematological“ syndromes in adult intensive care patients.
Vnitr Lek
; 68(8): 498-507, 2022.
Article
em En
| MEDLINE
| ID: mdl-36575067
ABSTRACT
Haemophagocytic syndrome, diffuse alveolar haemorrhage, catastrophic antiphospholipid syndrome and various types of thrombotic microangiopathies are rare conditions with significant morbidity and mortality. A common feature is late diagnosis, which can affect the success of treatment. The aim of this review article is to summarize the basic diagnostic and therapeutic steps of the present subpopulation of critically ill patients.
Palavras-chave
HLH; Lens-Associated Uveitis; antiphospholipid syndrome; antiglomerular basement membrane (antiGBM) antibodies; caplacizumab; catastrophic antiphospholipid syndrome; cytokine storm syndrome; diffuse alveolar haemorrhage; eculizumab; eculizumab; etoposide; haemolyticuremic syndrome; hemophagocytic lymphohistiocytosis; hemophagocytic syndrome; immunosuppressive therapy; macrophage activation syndrome; plasma exchange; ravulizumab; recombinant factor VIIa; rituximab; thrombosis; thrombotic microangiopathies; thrombotic microangiopathy; thrombotic thrombocytopenic purpura; vasculitis
Texto completo:
1
Base de dados:
MEDLINE
Assunto principal:
Síndrome Antifosfolipídica
/
Linfo-Histiocitose Hemofagocítica
/
Microangiopatias Trombóticas
Tipo de estudo:
Diagnostic_studies
Limite:
Adult
/
Humans
Idioma:
En
Ano de publicação:
2022
Tipo de documento:
Article