[Evoked potentials in 3 cases of dystrophia myotonica with neuropathic variant]. / Studio dei potenziali evocati in tre casi di distrofia miotonica con variante neuropatica.

ABSTRACT

3 patients with Myotonic Dystrophy (MD) and associated leg motor neuropathy, confirmed in two of them by biopsy of one branch of lateral popliteal nerve, were studied with Multimodality Evoked Potentials. Abnormalities of VEPs and BAEPs, in agreement with literature, were found in all patients. Median SEP peripheral conduction velocity, N9-N13 and N13-N20 conduction time were normal. On the contrary, all patients showed reduced lower limb SEP peripheral conduction velocity niloutstanding normal nerve biopsy. These results suggest in MD neurological abnormalities occur outside muscular system, too.