Secondary somatic glioblastoma arising from a mature ovarian cystic teratoma in a patient with underlying Li-Fraumeni syndrome.
Gynecol Oncol Rep
; 49: 101279, 2023 Oct.
Article
em En
| MEDLINE
| ID: mdl-37840845
ABSTRACT
â¢First report of a secondary somatic glioblastoma arising from MCT-MT in a patient with underlying Li-Fraumeni syndrome.â¢The rarity of glioblastoma arising from MCT-MT warrants investigation for underlying genetic predisposition.â¢Glioblastomas arising from MCT-MT appear to exhibit wild type IDH gene status.â¢Advanced-stage glioblastoma arising from MCT-MT exhibits aggressive behavior and requires adjuvant therapy.â¢Optimal adjuvant therapy regimen for glioblastoma arising from MCT-MT remains unknown.
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MEDLINE
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En
Ano de publicação:
2023
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Article