Concurrent renal and hepatic angiomyolipoma with pulmonary involvement in two patients with tuberous sclerosis / 대한내과학회지
Korean Journal of Medicine
; : 705-709, 2010.
Article
em Ko
| WPRIM
| ID: wpr-108495
Biblioteca responsável:
WPRO
ABSTRACT
Tuberous sclerosis (TS) involves multiple organs. Angiomyolipoma of the liver or kidney is one of the clinical manifestations of TS. However, coexistent renal and hepatic angiomyolipoma associated with TS is a rare condition. Pulmonary involvement is extremely rare, and occurs in only 0.1~1% of TS. We report two cases of concurrent renal and hepatic angiomyolipomas with pulmonary involvement in patients with TS. The first case was a 35 year-old woman who showed multiple angiomyolipomas in the liver and both kidneys and cystic parenchymal changes in the lungs. The other case was a 27-year-old woman who showed multiple angiomyolipomas in the liver and both kidneys, and multinodular pulmonary shadows. To the best of our knowledge, this is the first reported case of renal and hepatic angiomyolipomas associated with pulmonary involvement in Korea.
Palavras-chave
Texto completo:
1
Base de dados:
WPRIM
Assunto principal:
Esclerose Tuberosa
/
Linfangioleiomiomatose
/
Angiomiolipoma
/
Rim
/
Coreia (Geográfico)
/
Fígado
/
Pulmão
Limite:
Adult
/
Female
/
Humans
País como assunto:
Asia
Idioma:
Ko
Ano de publicação:
2010
Tipo de documento:
Article