A Case of a Calcitonin-Secreting Pancreatic Endocrine Tumor in a Pateint with Multiple Endocrine Neoplasia Type 1 / 대한내과학회지
Korean Journal of Medicine
; : 817-822, 2012.
Article
em Ko
| WPRIM
| ID: wpr-126590
Biblioteca responsável:
WPRO
ABSTRACT
Multiple endocrine neoplasia type 1 (MEN1) is an autosomal dominant hereditary disorder characterized by the combined occurrence of tumors of the parathyroid gland, exocrine pancreas, and anterior pituitary gland. Calcitonin-secreting pancreatic endocrine tumors are rare, and calcitonin-secreting pancreatic endocrine tumors with MEN1 have not been reported in Korea. A 46-year-old woman was admitted for a right breast cancer operation. Abnormal blood chemistry findings were hypercalcemia and elevated calcitonin. The patient was diagnosed with a calcitonin-secreting pancreatic endocrine tumor, left thyroid papillary carcinoma, right breast invasive ductal carcinoma, a thymic carcinoid tumor, left adrenal adenoma, uterine myoma, and adenomyosis by computed tomography scan, and with pituitary macroadenoma by brain magnetic resonance imaging. We present this case with a review of the literature, because it is the first reported calcitonin-secreting pancreatic endocrine tumor with MEN 1 in Korea.
Palavras-chave
Texto completo:
1
Base de dados:
WPRIM
Assunto principal:
Glândulas Paratireoides
/
Adeno-Hipófise
/
Glândula Tireoide
/
Encéfalo
/
Mama
/
Neoplasias da Mama
/
Calcitonina
/
Neoplasia Endócrina Múltipla
/
Imageamento por Ressonância Magnética
/
Tumor Carcinoide
Limite:
Female
/
Humans
País como assunto:
Asia
Idioma:
Ko
Ano de publicação:
2012
Tipo de documento:
Article